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    OpenPayerBilling CodesSystemic connective tissue disordersICD-10-CM m30-polyarteritis-nodosa-and-related-conditions
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    ICD-10-CM Code For Polyarteritis Nodosa And Related Conditions: Group Overview

    The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group M30 includes systemic necrotizing vasculitides such as polyarteritis nodosa and related medium-vessel vasculitis that can affect skin, nerves, kidneys, and visceral organs. These ICD-10-CM diagnosis codes are used to document clinical manifestations, organ involvement, and complications of medium-vessel vasculitis, capturing disease severity and systemic impact. Accurate coding within the ICD-10-CM M30 group supports complete clinical documentation and appropriate reimbursement.

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    ICD-10-CM M30: Polyarteritis Nodosa And Related Conditions Overview

    The ICD-10-CM M30 group encompasses systemic necrotizing vasculitides such as polyarteritis nodosa and related medium-vessel vasculitis disorders that affect multiple organ systems. These diagnoses target the vascular system and can involve skin, peripheral nerves, kidneys, gastrointestinal tract, and other organs. Accurate coding matters for clinical documentation and reimbursement because it reflects disease severity, organ involvement, and care complexity.

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    When to Use

    Use a code from this group when a clinician documents polyarteritis nodosa or a related medium-vessel vasculitis diagnosis with recorded organ involvement or complications. Select the code that best reflects the confirmed diagnosis and documented manifestations such as renal, neurologic, dermatologic, or gastrointestinal involvement.

    ICD-10-CM Codes

    5 rows

    ICD-10-CM CodeDescription
    M30.0Polyarteritis nodosa
    M30.1Polyarteritis with lung involvement [Churg-Strauss]
    M30.2Juvenile polyarteritis
    M30.3Mucocutaneous lymph node syndrome [Kawasaki]
    M30.8Other conditions related to polyarteritis nodosa

    DRG Codes

    6 rows

    DRG CodeDescription
    542Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy with MCC
    543Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy with CC
    544Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy without CC/MCC
    545Connective Tissue Disorders with MCC
    546Connective Tissue Disorders with CC
    547Connective Tissue Disorders without CC/MCC

    Typical Clinical Scenarios

    • A middle-aged adult presents to the emergency department with sudden-onset high fevers, diffuse myalgias, abdominal pain with melena, and new-onset mononeuropathy affecting the foot drop. Workup shows elevated inflammatory markers, hepatitis B surface antigen positivity, and angiographic evidence of medium-vessel aneurysms; biopsy of a mesenteric artery demonstrates transmural necrotizing inflammation and fibrinoid necrosis. A systemic necrotizing vasculitis of medium-sized arteries is diagnosed, leading to hospitalization for immunosuppression and management of organ-threatening inflammation. Typical codes: M30.0
    • An adolescent with a several-month history of migratory arthralgias, intermittent low-grade fever, livedo reticularis on the lower extremities, and progressive peripheral neuropathy (sensory loss in a stocking distribution) is evaluated in rheumatology clinic. Laboratory tests show raised ESR/CRP and negative serologies for ANCA; nerve biopsy reveals vasculitic changes consistent with polyarteritis nodosa–like medium-vessel vasculitis. A chronic systemic medium-vessel vasculitis diagnosis is assigned for outpatient immunomodulatory management and monitoring. Typical codes: M30.1
    • An older adult with long-standing systemic vasculitis develops chronic renal impairment and stage 3 chronic kidney disease attributed to prior ischemic injury from medium-vessel vasculitis; the patient is seen for nephrology follow-up for management of the renal sequelae. The visit documents the late sequelae of prior necrotizing medium-vessel vasculitis causing chronic organ damage rather than active systemic inflammation. Typical codes: M30.3, M30.8

    Related Codes

    M31-OTHER-NECROTIZING-VASCULOPATHIES

    ICD-10-CM Code For Other Necrotizing Vasculopathies: Group Overview

    M32-SYSTEMIC-LUPUS-ERYTHEMATOSUS

    ICD-10-CM Code For Systemic Lupus Erythematosus SLE: Group Overview

    M33-DERMATOPOLYMYOSITIS-CONDITIONS

    ICD-10-CM Code For Dermatopolymyositis: Group Overview

    M34-SYSTEMIC-SCLEROSIS-SCLERODERMA

    ICD-10-CM Code For Systemic Sclerosis [Scleroderma]: Group Overview

    M35-OTHER-SYSTEMIC-INVOLVEMENT-OF-CONNECTIVE-TISSUE

    ICD-10-CM Code For Other Systemic Involvement Of Connective Tissue: Group Overview

    M36-SYSTEMIC-CONNECTIVE-TISSUE-DISORDERS

    ICD-10-CM Code For Systemic Disorders Of Connective Tissue In Diseases Classified Elsewhere: Group Overview

    Frequently Asked Questions

    References

    1. 1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
    2. 2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
    3. 3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.
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