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    v1.0.28
    OpenPayerBilling CodesGlomerular diseasesICD-10-CM n07-hereditary-nephropathy-not-elsewhere-classified
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    ICD-10-CM Code For Hereditary Nephropathy Not Elsewhere Classified: Group Overview

    The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group N07 includes hereditary glomerular disorders not classified elsewhere, such as inherited nephropathies causing proteinuria, hematuria, and progressive renal impairment. These ICD-10-CM diagnosis codes are used to document hereditary renal diseases with glomerular involvement, capturing disease severity, organ involvement, or clinical complexity relevant to this group. Accurate coding within the ICD-10-CM N07 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

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    ICD-10-CM N07: Hereditary Nephropathy, Not Elsewhere Classified Overview

    This group comprises hereditary glomerular disorders that primarily affect the kidney's filtering units and are not classified elsewhere. It targets inherited nephropathies with glomerular involvement resulting in proteinuria, hematuria, or progressive renal dysfunction. Accurate coding matters because it supports appropriate clinical documentation and influences reimbursement and care coordination.

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    When to Use

    Use a code from this group when a documented hereditary glomerular disorder is the primary diagnosis and no more specific hereditary kidney disease code applies. Codes from this group are selected to reflect the documented clinical features, disease severity, and organ involvement at the time of encounter.

    ICD-10-CM Codes

    12 rows

    ICD-10-CM CodeDescription
    N07.0Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
    N07.1Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
    N07.2Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis
    N07.3Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis
    N07.4Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis
    N07.5Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis
    N07.6Hereditary nephropathy, not elsewhere classified with dense deposit disease
    N07.7Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis
    N07.8Hereditary nephropathy, not elsewhere classified with other morphologic lesions
    N07.9Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions
    N07.AHereditary nephropathy, not elsewhere classified with C3 glomerulonephritis
    N07.BHereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD]

    DRG Codes

    3 rows

    DRG CodeDescription
    698Other Kidney and Urinary Tract Diagnoses with MCC
    699Other Kidney and Urinary Tract Diagnoses with CC
    700Other Kidney and Urinary Tract Diagnoses without CC/MCC

    Typical Clinical Scenarios

    • An adolescent with a known family history of Alport syndrome presents to nephrology with progressive hematuria, persistent proteinuria on urinalysis, and declining renal function over months despite conservative management. Genetic testing and renal biopsy confirm hereditary nephropathy with features of hereditary nephritis, prompting assignment of a hereditary glomerular disease code to capture the inherited etiology and chronic progression. Typical codes: N07.0, N07.1
    • An adult patient presents to the emergency department with sudden onset edema, marked proteinuria in the nephrotic range, and acute kidney injury after a recent diagnosis of familial focal segmental glomerulosclerosis in the family; biopsy supports a hereditary pattern of glomerular injury. The acute presentation with nephrotic syndrome superimposed on an inherited glomerulopathy leads to coding from this hereditary nephropathy group to reflect both the genetic basis and the current nephrotic/acute course. Typical codes: N07.2, N07.3
    • A middle-aged patient with long-standing hereditary glomerular disease is admitted for management of end-stage renal disease and is undergoing evaluation for dialysis access placement and transplant listing; chart documents chronic hereditary nephritis as the cause of the patient’s ESRD and comorbid hypertension. Use of a code from this hereditary group documents the underlying inherited glomerular disorder as the etiology of chronic kidney disease contributing to current care and comorbid management. Typical codes: N07.8, N07.9

    Related Codes

    N00-ACUTE-NEPHRITIC-SYNDROME

    ICD-10-CM Code For Acute Nephritic Syndrome: Group Overview

    N01-RAPIDLY-PROGRESSIVE-NEPHRITIC-SYNDROME

    ICD-10-CM Code For Rapidly Progressive Nephritic Syndrome: Group Overview

    N02-RECURRENT-AND-PERSISTENT-HEMATURIA

    ICD-10-CM Code For Recurrent And Persistent Hematuria: Group Overview

    N03-CHRONIC-NEPHRITIC-SYNDROME

    ICD-10-CM Code For Chronic Nephritic Syndrome: Group Overview

    N04-NEPHROTIC-SYNDROME

    ICD-10-CM Code For Nephrotic Syndrome: Group Overview

    N05-UNSPECIFIED-NEPHRITIC-SYNDROME

    ICD-10-CM Code For Unspecified Nephritic Syndrome: Group Overview

    N06-ISOLATED-PROTEINURIA-WITH-LESION

    ICD-10-CM Code For Isolated Proteinuria With Specified Morphological Lesion: Group Overview

    N08-GLOMERULAR-DISORDERS-IN-DISEASES-CLASSIFIED-ELSEWHERE

    ICD-10-CM Code For Glomerular Disorders In Diseases Classified Elsewhere: Group Overview

    Frequently Asked Questions

    References

    1. 1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
    2. 2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
    3. 3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.
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