ICD-10-CM Code For Other Pulmonary Heart Diseases: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group I27 includes disorders of the pulmonary circulation and pulmonary heart disease other than primary pulmonary hypertension, such as chronic thromboembolic pulmonary hypertension and other secondary pulmonary hypertensive conditions. These ICD-10-CM diagnosis codes are used to document clinical scenarios involving elevated pulmonary arterial pressure due to thromboembolic disease, lung or heart disease, or other identifiable causes, capturing disease severity, organ involvement, or clinical complexity relevant to this group. Accurate coding within the ICD-10-CM I27 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

Customize your policy alerts

Sign up for ICD-10-CM Code For Other Pulmonary Heart Diseases: Group Overview policy alerts

Get alerted when relevant policies change without checking for updates manually.

Monitor payer policy activity

Receive email alerts as soon as relevant payer policies are published or updated.

ICD-10-CM I27: Other Pulmonary Heart Diseases Overview

The diagnoses in this group represent conditions affecting the pulmonary circulation and right heart function separate from primary pulmonary hypertension, including chronic thromboembolic and other secondary pulmonary hypertensive disorders. These conditions target the pulmonary vasculature and right-sided cardiac consequences, impacting respiratory and cardiovascular systems. Accurate coding matters for reimbursement because it documents disease complexity and guides appropriate claim processing and severity adjustment.

When to Use

Codes from this group are used when a clinician documents pulmonary hypertension or pulmonary heart disease attributed to identifiable causes such as chronic thromboembolic disease, lung disease, or left heart disease. Use these codes to capture the specific etiology and severity of pulmonary circulatory disorders when documented in the medical record.

ICD-10-CM Codes

17 rows

ICD-10-CM Code	Description
I27.0	Primary pulmonary hypertension
I27.1	Kyphoscoliotic heart disease
I27.20	Pulmonary hypertension, unspecified
I27.21	Secondary pulmonary arterial hypertension
I27.22	Pulmonary hypertension due to left heart disease
I27.23	Pulmonary hypertension due to lung diseases and hypoxia
I27.24	Chronic thromboembolic pulmonary hypertension
I27.29	Other secondary pulmonary hypertension
I27.81	Cor pulmonale (chronic)
I27.82	Chronic pulmonary embolism
I27.83	Eisenmenger's syndrome
I27.840	Fontan-associated liver disease [FALD]
I27.841	Fontan-associated lymphatic dysfunction
I27.848	Other Fontan-associated condition
I27.849	Fontan related circulation, unspecified
I27.89	Other specified pulmonary heart diseases
I27.9	Pulmonary heart disease, unspecified

DRG Codes

14 rows

DRG Code	Description
173	Ultrasound Accelerated and Other Thrombolysis with Principal Diagnosis Pulmonary Embolism
175	Pulmonary Embolism with MCC or Acute Cor Pulmonale
176	Pulmonary Embolism without MCC
314	Other Circulatory System Diagnoses with MCC
315	Other Circulatory System Diagnoses with CC
316	Other Circulatory System Diagnoses without CC/MCC
441	Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with MCC
442	Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with CC
443	Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis without CC/MCC
791	Prematurity with Major Problems
793	Full Term Neonate with Major Problems
808	Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC
809	Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC
810	Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC

Typical Clinical Scenarios

A 65-year-old patient with long-standing chronic obstructive pulmonary disease presents with progressive exertional dyspnea, lower extremity edema, and jugular venous distention; echocardiography shows right ventricular dilation and reduced right ventricular function consistent with cor pulmonale due to chronic lung disease, and the clinician documents chronic pulmonary heart disease as the primary cardiac complication of the pulmonary disorder. This represents a chronic, progressive condition secondary to chronic hypoxic lung disease where a code for right heart involvement from pulmonary disease is assigned. Typical codes: I27.8, I27.89
A 54-year-old woman is admitted from the emergency department with sudden severe shortness of breath, pleuritic chest pain, tachycardia, and hypoxemia after recent hip fracture surgery; imaging demonstrates acute pulmonary embolism with signs of acute right ventricular strain, and the treating team documents acute pulmonary heart disease/acute cor pulmonale. This is an acute, emergency presentation where a pulmonary vascular obstruction has led to acute compromise of right heart function and an acute pulmonary circulation diagnosis is used. Typical codes: I27.0, I27.2
A 48-year-old patient with systemic sclerosis followed in clinic reports progressive dyspnea on exertion and a recent decline in six-minute walk distance; right heart catheterization confirms pulmonary arterial hypertension attributed to connective tissue disease, and the visit documents pulmonary arterial hypertension as a chronic pulmonary circulation disorder requiring ongoing therapy and surveillance. This is a chronic comorbidity of a systemic disease where a specific pulmonary hypertension code is assigned for management and longitudinal care. Typical codes: I27.20, I27.21

Related Codes

I26-PULMONARY-EMBOLISM

ICD-10-CM Code For Pulmonary Embolism: Group Overview

I28-OTHER-DISEASES-OF-PULMONARY-VESSELS

ICD-10-CM Code For Other Diseases Of Pulmonary Vessels: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

Trek Health ingests and normalizes Transparency in Coverage data and payer policy updates to give provider organizations a clear view of how commercial reimbursement behaves across markets, payers, and services. Our platform transforms raw payer disclosures into structured intelligence that supports contract evaluation, payer negotiations, and service line strategy. By combining market benchmarks with ongoing policy visibility, Trek helps teams identify variability, risk, and opportunity in commercial reimbursement. The result is faster insight, stronger negotiating positions, and more informed financial decisions.

Explore openpayer tools

View all tools

When to Use

ICD-10-CM Codes

17 rows

ICD-10-CM Code	Description
I27.0	Primary pulmonary hypertension
I27.1	Kyphoscoliotic heart disease
I27.20	Pulmonary hypertension, unspecified
I27.21	Secondary pulmonary arterial hypertension
I27.22	Pulmonary hypertension due to left heart disease
I27.23	Pulmonary hypertension due to lung diseases and hypoxia
I27.24	Chronic thromboembolic pulmonary hypertension
I27.29	Other secondary pulmonary hypertension
I27.81	Cor pulmonale (chronic)
I27.82	Chronic pulmonary embolism
I27.83	Eisenmenger's syndrome
I27.840	Fontan-associated liver disease [FALD]
I27.841	Fontan-associated lymphatic dysfunction
I27.848	Other Fontan-associated condition
I27.849	Fontan related circulation, unspecified
I27.89	Other specified pulmonary heart diseases
I27.9	Pulmonary heart disease, unspecified

DRG Codes

14 rows

DRG Code	Description
173	Ultrasound Accelerated and Other Thrombolysis with Principal Diagnosis Pulmonary Embolism
175	Pulmonary Embolism with MCC or Acute Cor Pulmonale
176	Pulmonary Embolism without MCC
314	Other Circulatory System Diagnoses with MCC
315	Other Circulatory System Diagnoses with CC
316	Other Circulatory System Diagnoses without CC/MCC
441	Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with MCC
442	Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with CC
443	Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis without CC/MCC
791	Prematurity with Major Problems
793	Full Term Neonate with Major Problems
808	Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with MCC
809	Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders with CC
810	Major Hematological and Immunological Diagnoses Except Sickle Cell Crisis and Coagulation Disorders without CC/MCC

Typical Clinical Scenarios

A 65-year-old patient with long-standing chronic obstructive pulmonary disease presents with progressive exertional dyspnea, lower extremity edema, and jugular venous distention; echocardiography shows right ventricular dilation and reduced right ventricular function consistent with cor pulmonale due to chronic lung disease, and the clinician documents chronic pulmonary heart disease as the primary cardiac complication of the pulmonary disorder. This represents a chronic, progressive condition secondary to chronic hypoxic lung disease where a code for right heart involvement from pulmonary disease is assigned. Typical codes: I27.8, I27.89
A 54-year-old woman is admitted from the emergency department with sudden severe shortness of breath, pleuritic chest pain, tachycardia, and hypoxemia after recent hip fracture surgery; imaging demonstrates acute pulmonary embolism with signs of acute right ventricular strain, and the treating team documents acute pulmonary heart disease/acute cor pulmonale. This is an acute, emergency presentation where a pulmonary vascular obstruction has led to acute compromise of right heart function and an acute pulmonary circulation diagnosis is used. Typical codes: I27.0, I27.2
A 48-year-old patient with systemic sclerosis followed in clinic reports progressive dyspnea on exertion and a recent decline in six-minute walk distance; right heart catheterization confirms pulmonary arterial hypertension attributed to connective tissue disease, and the visit documents pulmonary arterial hypertension as a chronic pulmonary circulation disorder requiring ongoing therapy and surveillance. This is a chronic comorbidity of a systemic disease where a specific pulmonary hypertension code is assigned for management and longitudinal care. Typical codes: I27.20, I27.21

Related Codes

I26-PULMONARY-EMBOLISM

ICD-10-CM Code For Pulmonary Embolism: Group Overview

I28-OTHER-DISEASES-OF-PULMONARY-VESSELS

ICD-10-CM Code For Other Diseases Of Pulmonary Vessels: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Other Pulmonary Heart Diseases: Group Overview

Sign up for ICD-10-CM Code For Other Pulmonary Heart Diseases: Group Overview policy alerts

ICD-10-CM I27: Other Pulmonary Heart Diseases Overview

ICD-10-CM Code For Other Pulmonary Heart Diseases: Group Overview

Sign up for ICD-10-CM Code For Other Pulmonary Heart Diseases: Group Overview policy alerts

ICD-10-CM I27: Other Pulmonary Heart Diseases Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which ICD-10-CM codes are included in the I27 group for other pulmonary heart diseases?

What clinical scenarios are documented using ICD-10-CM I27 codes?

How does accurate coding within the I27 group affect reimbursement and claims?

Which DRGs are related to conditions in the I27 group that coders should be aware of?

Which I27 codes specify Fontan-associated conditions and how are they represented?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which ICD-10-CM codes are included in the I27 group for other pulmonary heart diseases?

What clinical scenarios are documented using ICD-10-CM I27 codes?

How does accurate coding within the I27 group affect reimbursement and claims?

Which DRGs are related to conditions in the I27 group that coders should be aware of?

Which I27 codes specify Fontan-associated conditions and how are they represented?

References