ICD-10-CM Code For Other Diseases Of Pulmonary Vessels: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group I28 includes nonhypertensive pulmonary vascular diseases such as pulmonary embolism sequelae, pulmonary vascular stenosis, and other specified diseases of the pulmonary vessels that affect pulmonary circulation and right heart function. These ICD-10-CM diagnosis codes are used to document clinical presentations involving pulmonary vascular obstruction, chronic sequelae after embolic events, or other structural and functional pulmonary vascular disorders, capturing disease severity, organ involvement, or clinical complexity relevant to this group. Accurate coding within the ICD-10-CM I28 group supports proper claim adjudication and complete clinical documentation and appropriate reimbursement.

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ICD-10-CM I28: Other Diseases Of Pulmonary Vessels Overview

The diagnoses in this group represent non-hypertensive and other specified diseases affecting the pulmonary vessels, including various forms of pulmonary vascular obstruction and disease. These conditions target the pulmonary circulation and can impact right heart function and gas exchange. Accurate coding matters for reimbursement because it ensures clinical severity and complication status are properly documented for claims.

When to Use

Use a code from this group when documentation indicates a specific nonhypertensive pulmonary vascular disease such as chronic embolic changes, vascular stenosis, or other specified pulmonary vessel disorders. Select the code that best reflects the documented etiology, chronicity, and any sequelae or complications noted in the clinical record.

ICD-10-CM Codes

4 rows

ICD-10-CM Code	Description
I28.0	Arteriovenous fistula of pulmonary vessels
I28.1	Aneurysm of pulmonary artery
I28.8	Other diseases of pulmonary vessels
I28.9	Disease of pulmonary vessels, unspecified

DRG Codes

3 rows

DRG Code	Description
314	Other Circulatory System Diagnoses with MCC
315	Other Circulatory System Diagnoses with CC
316	Other Circulatory System Diagnoses without CC/MCC

Typical Clinical Scenarios

A 68-year-old patient with long-standing left-sided heart failure presents with progressive dyspnea on exertion, peripheral edema, and signs of right ventricular enlargement on echocardiogram consistent with cor pulmonale due to chronic left heart disease; the clinician documents a pulmonary vascular disease not specified as thromboembolic and assigns a code reflecting chronic pulmonary vascular involvement. Typical codes: I28.0, I28.9
A middle-aged patient with progressive exertional dyspnea, hypoxemia, and a workup including right heart catheterization confirming elevated pulmonary arterial pressures consistent with primary pulmonary hypertension or other chronic pulmonary arterial hypertension; the visit is for ongoing management of pulmonary vascular hypertension as a chronic condition. Typical codes: I28.0, I28.1
A patient hospitalized after an acute presentation of chest pain and sudden worsening dyspnea following recovery from a recent pulmonary embolism, found to have chronic thromboembolic changes of the pulmonary vasculature leading to secondary pulmonary vascular disease; the admission documents pulmonary vascular complications related to prior thromboembolism. Typical codes: I28.8, I28.9

Related Codes

I26-PULMONARY-EMBOLISM

ICD-10-CM Code For Pulmonary Embolism: Group Overview

I27-OTHER-PULMONARY-HEART-DISEASES

ICD-10-CM Code For Other Pulmonary Heart Diseases: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

4 rows

ICD-10-CM Code	Description
I28.0	Arteriovenous fistula of pulmonary vessels
I28.1	Aneurysm of pulmonary artery
I28.8	Other diseases of pulmonary vessels
I28.9	Disease of pulmonary vessels, unspecified

DRG Codes

3 rows

DRG Code	Description
314	Other Circulatory System Diagnoses with MCC
315	Other Circulatory System Diagnoses with CC
316	Other Circulatory System Diagnoses without CC/MCC

Typical Clinical Scenarios

A 68-year-old patient with long-standing left-sided heart failure presents with progressive dyspnea on exertion, peripheral edema, and signs of right ventricular enlargement on echocardiogram consistent with cor pulmonale due to chronic left heart disease; the clinician documents a pulmonary vascular disease not specified as thromboembolic and assigns a code reflecting chronic pulmonary vascular involvement. Typical codes: I28.0, I28.9
A middle-aged patient with progressive exertional dyspnea, hypoxemia, and a workup including right heart catheterization confirming elevated pulmonary arterial pressures consistent with primary pulmonary hypertension or other chronic pulmonary arterial hypertension; the visit is for ongoing management of pulmonary vascular hypertension as a chronic condition. Typical codes: I28.0, I28.1
A patient hospitalized after an acute presentation of chest pain and sudden worsening dyspnea following recovery from a recent pulmonary embolism, found to have chronic thromboembolic changes of the pulmonary vasculature leading to secondary pulmonary vascular disease; the admission documents pulmonary vascular complications related to prior thromboembolism. Typical codes: I28.8, I28.9

Related Codes

I26-PULMONARY-EMBOLISM

ICD-10-CM Code For Pulmonary Embolism: Group Overview

I27-OTHER-PULMONARY-HEART-DISEASES

ICD-10-CM Code For Other Pulmonary Heart Diseases: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Other Diseases Of Pulmonary Vessels: Group Overview

Sign up for ICD-10-CM Code For Other Diseases Of Pulmonary Vessels: Group Overview policy alerts

ICD-10-CM I28: Other Diseases Of Pulmonary Vessels Overview

ICD-10-CM Code For Other Diseases Of Pulmonary Vessels: Group Overview

Sign up for ICD-10-CM Code For Other Diseases Of Pulmonary Vessels: Group Overview policy alerts

ICD-10-CM I28: Other Diseases Of Pulmonary Vessels Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in ICD-10-CM code group I28?

What are the specific ICD-10-CM codes listed in this group?

How does accurate coding within I28 affect reimbursement?

Which DRGs are related to ICD-10-CM I28 diagnoses?

What clinical presentations are captured by the I28 code group?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in ICD-10-CM code group I28?

What are the specific ICD-10-CM codes listed in this group?

How does accurate coding within I28 affect reimbursement?

Which DRGs are related to ICD-10-CM I28 diagnoses?

What clinical presentations are captured by the I28 code group?

References