Loading...

    Explore
    • Policy Monitoring
    • Live Policy Feed
    • Billing Codes
    • NPI Medicare & Medicaid
    • Healthcare Providers
    • Health Insurance Payers
    • States
    • Service Lines
    • Taxonomy Codes
    Lookup tools
    • Billing Code Lookup
    • CPT Modifier Lookup
    • Provider Taxonomy Code Lookup
    • Healthcare Provider & Facility Lookup
    • Health Insurance Payer Lookup
    • Payer Contact Directory

    Policy & Benchmark Tools

    • Prior Authorization Lookup
    • Coverage Criteria Lookup
    • Timely Filing Lookup
    • Billing Code Reimbursement Rates
    • Payer Comparison Dashboard
    • Facility Comparison Dashboard
    • All tools

    Company

    • About OpenPayer
    • Data Sources
    • Trek Health
    OpenPayerby Trek Health
    LinkedInYouTube

    © 2026 Trek Health. All rights reserved.

    OpenPayer is built and maintained by Trek Health.

    v1.0.28
    OpenPayerBilling CodesAcute rheumatic feverICD-10-CM i00-rheumatic-fever-without-heart-involvement
    Ask Trek AI about this page

    ICD-10-CM Code For Rheumatic Fever Without Heart Involvement: Group Overview

    The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group I00 includes diagnoses for acute rheumatic fever without involvement of the heart, covering manifestations such as migratory polyarthritis, chorea, erythema marginatum, and subcutaneous nodules that arise after Group A streptococcal infection. These ICD-10-CM diagnosis codes are used to document clinical scenarios that distinguish noncarditic rheumatic fever from rheumatic fever with cardiac involvement, capturing disease manifestations, affected organ systems, and clinical complexity relevant to management. Accurate coding within the ICD-10-CM I00 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

    Customize your policy alerts

    Sign up for ICD-10-CM Code For Rheumatic Fever Without Heart Involvement: Group Overview policy alerts

    Get alerted when relevant policies change without checking for updates manually.

    Monitor payer policy activity

    Receive email alerts as soon as relevant payer policies are published or updated.

    ICD-10-CM I00: Rheumatic Fever Without Heart Involvement Overview

    This code group represents acute rheumatic fever cases that do not involve cardiac manifestations, typically following an untreated or inadequately treated Group A streptococcal infection. It targets inflammatory and migratory manifestations such as arthritis, chorea, and subcutaneous nodules affecting the musculoskeletal and nervous systems. Accurate coding is important for correct clinical documentation and for appropriate reimbursement related to treatment of noncarditic rheumatic fever.

    Table of contents

    Progress1 / 6

    Explore openpayer tools

    • Billing CodesCPT, HCPCS, DRG & more
    • Reimbursement RatesCommercial vs. Medicare rate reports
    • ProvidersHospitals & facilities
    • PayersPlans & market footprint
    • Taxonomy CodesNUCC specialty codes
    • ModifiersCPT modifiers & usage
    • Prior AuthorizationPA policies by payer & drug
    • Timely FilingFiling deadlines by payer
    • Coverage CriteriaMedical necessity by payer
    • Payer ContactsClaims, PA & appeals contacts
    View all tools

    When to Use

    Use a code from this group when a patient has clinical features of acute rheumatic fever without documented valvular or other cardiac involvement. Codes in this group apply when the diagnosis is confirmed clinically or by relevant testing and cardiac involvement has been excluded.

    ICD-10-CM Codes

    1 rows

    ICD-10-CM CodeDescription
    I00Rheumatic fever without heart involvement

    DRG Codes

    3 rows

    DRG CodeDescription
    545Connective Tissue Disorders with MCC
    546Connective Tissue Disorders with CC
    547Connective Tissue Disorders without CC/MCC

    Typical Clinical Scenarios

    • A school-aged child presents to the pediatric urgent care with abrupt onset fever, migratory polyarthritis affecting knees and ankles, and tender subcutaneous nodules after a documented group A streptococcal pharyngitis two weeks prior. The clinician documents acute systemic inflammatory signs with no evidence of carditis on exam or echocardiography, and the diagnosis is assigned for post-streptococcal rheumatic fever without cardiac involvement. Typical codes: I00
    • An adolescent is hospitalized for severe choreiform movements (Sydenham chorea), emotional lability, and recent history of untreated strep throat; cardiac evaluation including ECG and echocardiogram shows no valvular disease. Neurological manifestations of acute rheumatic fever are the primary reason for admission, and the rheumatologic diagnosis without heart involvement is recorded to capture the acute extra-cardiac manifestation. Typical codes: I00
    • An adult presents to an outpatient rheumatology clinic for follow-up three weeks after being treated for acute streptococcal pharyngitis; they report migratory joint pains and low-grade fever but prior cardiology workup was negative for carditis. The visit documents ongoing acute rheumatic inflammatory activity limited to joints and soft tissues without cardiac sequelae, so the code for rheumatic fever without heart involvement is assigned for outpatient management and surveillance. Typical codes: I00

    Related Codes

    I01-RHEUMATIC-FEVER-WITH-HEART-INVOLVEMENT

    ICD-10-CM Code For Rheumatic Fever With Heart Involvement: Group Overview

    I02-RHEUMATIC-CHOREA

    ICD-10-CM Code For Rheumatic Chorea: Group Overview

    Frequently Asked Questions

    References

    1. 1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
    2. 2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
    3. 3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.
    Published by

    Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

    Trek Health ingests and normalizes Transparency in Coverage data and payer policy updates to give provider organizations a clear view of how commercial reimbursement behaves across markets, payers, and services. Our platform transforms raw payer disclosures into structured intelligence that supports contract evaluation, payer negotiations, and service line strategy. By combining market benchmarks with ongoing policy visibility, Trek helps teams identify variability, risk, and opportunity in commercial reimbursement. The result is faster insight, stronger negotiating positions, and more informed financial decisions.