ICD-10-CM Code For Rheumatic Fever With Heart Involvement: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group I01 includes acute rheumatic fever with cardiac involvement such as rheumatic carditis, valvulitis, and other heart-related manifestations following streptococcal infection. These ICD-10-CM diagnosis codes are used to document clinical scenarios involving active rheumatic inflammation of the heart, capturing severity, specific cardiac structures affected, and associated clinical complexity. Accurate coding within the ICD-10-CM I01 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

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ICD-10-CM I01: Rheumatic Fever With Heart Involvement Overview

The diagnoses in this group represent acute rheumatic fever affecting the heart, including carditis and other cardiac manifestations resulting from a poststreptococcal inflammatory process. These conditions target the cardiovascular system and can involve valvular, myocardial, or pericardial inflammation. Accurate coding matters for reimbursement because it reflects disease severity and organ involvement, which affect claim adjudication and payment.

When to Use

Use a code from this group when a patient is diagnosed with acute rheumatic fever that specifically involves the heart, such as documented carditis or valvulitis after streptococcal infection. Select the code that reflects the specific cardiac structures affected and the clinical severity documented in the medical record.

ICD-10-CM Codes

5 rows

ICD-10-CM Code	Description
I01.0	Acute rheumatic pericarditis
I01.1	Acute rheumatic endocarditis
I01.2	Acute rheumatic myocarditis
I01.8	Other acute rheumatic heart disease
I01.9	Acute rheumatic heart disease, unspecified

DRG Codes

5 rows

DRG Code	Description
306	Cardiac Congenital and Valvular Disorders with MCC
307	Cardiac Congenital and Valvular Disorders without MCC
314	Other Circulatory System Diagnoses with MCC
315	Other Circulatory System Diagnoses with CC
316	Other Circulatory System Diagnoses without CC/MCC

Typical Clinical Scenarios

A previously healthy adolescent presents to the emergency department with high fever, migratory polyarthritis of the knees and ankles, and choreiform movements after a recent untreated streptococcal pharyngitis. Emergency clinicians document active systemic inflammatory findings and suspect acute rheumatic fever with carditis based on tachycardia, a new holosystolic murmur, and elevated inflammatory markers; a diagnosis from this group is assigned to capture the acute rheumatic process with heart involvement. Typical codes: I01.0, I01.1
An adult patient with known rheumatic valvular disease is seen in cardiology clinic for progressive dyspnea and echocardiography showing mitral regurgitation thought to be due to prior rheumatic carditis; the visit documents chronic valvular dysfunction attributable to rheumatic fever. Because the encounter addresses rheumatic heart sequelae and possible ongoing inflammatory activity, a code from this group is used to indicate rheumatic fever affecting the heart as the underlying cause. Typical codes: I01.2, I01.9
A pediatric inpatient admitted with congestive heart failure symptoms after an acute presentation of fever and migratory arthritis is found to have rheumatic pancarditis with pericardial involvement and clinical heart failure requiring diuretics and monitoring. The admission diagnosis specifies rheumatic fever with combined cardiac manifestations reflecting acute, severe involvement of the myocardium and pericardium, so an appropriate code from this group is assigned to document the rheumatic cardiac complication. Typical codes: I01.8, I01.1

ICD-10-CM Code For Rheumatic Fever Without Heart Involvement: Group Overview

I02-RHEUMATIC-CHOREA

ICD-10-CM Code For Rheumatic Chorea: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

5 rows

ICD-10-CM Code	Description
I01.0	Acute rheumatic pericarditis
I01.1	Acute rheumatic endocarditis
I01.2	Acute rheumatic myocarditis
I01.8	Other acute rheumatic heart disease
I01.9	Acute rheumatic heart disease, unspecified

DRG Codes

5 rows

DRG Code	Description
306	Cardiac Congenital and Valvular Disorders with MCC
307	Cardiac Congenital and Valvular Disorders without MCC
314	Other Circulatory System Diagnoses with MCC
315	Other Circulatory System Diagnoses with CC
316	Other Circulatory System Diagnoses without CC/MCC

Typical Clinical Scenarios

A previously healthy adolescent presents to the emergency department with high fever, migratory polyarthritis of the knees and ankles, and choreiform movements after a recent untreated streptococcal pharyngitis. Emergency clinicians document active systemic inflammatory findings and suspect acute rheumatic fever with carditis based on tachycardia, a new holosystolic murmur, and elevated inflammatory markers; a diagnosis from this group is assigned to capture the acute rheumatic process with heart involvement. Typical codes: I01.0, I01.1
An adult patient with known rheumatic valvular disease is seen in cardiology clinic for progressive dyspnea and echocardiography showing mitral regurgitation thought to be due to prior rheumatic carditis; the visit documents chronic valvular dysfunction attributable to rheumatic fever. Because the encounter addresses rheumatic heart sequelae and possible ongoing inflammatory activity, a code from this group is used to indicate rheumatic fever affecting the heart as the underlying cause. Typical codes: I01.2, I01.9
A pediatric inpatient admitted with congestive heart failure symptoms after an acute presentation of fever and migratory arthritis is found to have rheumatic pancarditis with pericardial involvement and clinical heart failure requiring diuretics and monitoring. The admission diagnosis specifies rheumatic fever with combined cardiac manifestations reflecting acute, severe involvement of the myocardium and pericardium, so an appropriate code from this group is assigned to document the rheumatic cardiac complication. Typical codes: I01.8, I01.1

ICD-10-CM Code For Rheumatic Fever Without Heart Involvement: Group Overview

I02-RHEUMATIC-CHOREA

ICD-10-CM Code For Rheumatic Chorea: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Rheumatic Fever With Heart Involvement: Group Overview

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ICD-10-CM I01: Rheumatic Fever With Heart Involvement Overview

ICD-10-CM Code For Rheumatic Fever With Heart Involvement: Group Overview

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ICD-10-CM I01: Rheumatic Fever With Heart Involvement Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

References

ICD-10-CM Code For Rheumatic Fever With Heart Involvement: Group Overview

Sign up for ICD-10-CM Code For Rheumatic Fever With Heart Involvement: Group Overview policy alerts

ICD-10-CM I01: Rheumatic Fever With Heart Involvement Overview

ICD-10-CM Code For Rheumatic Fever With Heart Involvement: Group Overview

Sign up for ICD-10-CM Code For Rheumatic Fever With Heart Involvement: Group Overview policy alerts

ICD-10-CM I01: Rheumatic Fever With Heart Involvement Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which diagnoses are included in the ICD-10-CM I01 group for rheumatic fever with heart involvement?

Why does accurate coding within the `I01` group matter for reimbursement?

What types of cardiac involvement are described by the I01 code group?

Which DRGs are related to the I01 diagnoses for billing and grouping purposes?

How do the I01 codes capture clinical complexity for documentation?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which diagnoses are included in the ICD-10-CM I01 group for rheumatic fever with heart involvement?

Why does accurate coding within the `I01` group matter for reimbursement?

What types of cardiac involvement are described by the I01 code group?

Which DRGs are related to the I01 diagnoses for billing and grouping purposes?

How do the I01 codes capture clinical complexity for documentation?

References