ICD-10-CM Code For Pemphigoid: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group L12 includes autoimmune subepidermal blistering disorders such as bullous pemphigoid and related pemphigoid variants that primarily affect the skin and mucous membranes. These ICD-10-CM diagnosis codes are used to document clinical scenarios including blistering severity, extent of skin and mucosal involvement, and complications such as secondary infection or scarring. Accurate coding within the ICD-10-CM L12 group supports proper claim adjudication and appropriate reimbursement.

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ICD-10-CM L12: Pemphigoid Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM L12) pemphigoid group represents autoimmune subepidermal blistering disorders that primarily affect the skin and mucous membranes. These conditions target the integumentary system and can lead to tense blisters, erosions, and potential mucosal involvement. Accurate coding matters for appropriate claim adjudication and to reflect disease severity and treatment needs for reimbursement.

When to Use

Use a code from this group when the clinical record documents a diagnosis of pemphigoid or a specified pemphigoid variant with evidence of blistering disease. Select the most specific code that reflects the site involvement, severity, and any documented complications.

ICD-10-CM Codes

8 rows

ICD-10-CM Code	Description
L12.0	Bullous pemphigoid
L12.1	Cicatricial pemphigoid
L12.2	Chronic bullous disease of childhood
L12.30	Acquired epidermolysis bullosa, unspecified
L12.31	Epidermolysis bullosa due to drug
L12.35	Other acquired epidermolysis bullosa
L12.8	Other pemphigoid
L12.9	Pemphigoid, unspecified

DRG Codes

4 rows

DRG Code	Description
595	Major Skin Disorders with MCC
596	Major Skin Disorders without MCC
606	Minor Skin Disorders with MCC
607	Minor Skin Disorders without MCC

Typical Clinical Scenarios

An elderly patient presents to the emergency department with sudden onset of widespread tense blisters and pruritic urticarial plaques over the trunk and limbs, some of which have eroded and caused serous drainage; the patient reports progressive skin separation over days and mild oral mucosal involvement. The acute presentation with characteristic tense bullae and mucosal lesions prompts diagnosis and inpatient dermatology evaluation, and a bullous pemphigoid spectrum code is assigned. Typical codes: L12.0, L12.1
A middle-aged patient is seen in dermatology clinic for chronic, relapsing subepidermal blistering limited to the oral mucosa and conjunctiva, with scarring and symblepharon formation after repeated flares despite topical therapy. This represents a chronic cicatricial mucous membrane–predominant autoimmune blistering disease requiring ongoing management, and a mucous membrane–predominant pemphigoid code is used. Typical codes: L12.31, L12.35
A patient with longstanding bullous disease presents to primary care with secondary skin infection of ruptured bullae, fever, and cellulitis around multiple lesion sites; the visit documents an infectious complication of an underlying blistering disorder. Coding reflects the underlying bullous condition with notation for complications of blistering disease as applicable. Typical codes: L12.8, L12.9

Related Codes

L10-PEMPHIGUS

ICD-10-CM Code For Pemphigus: Group Overview

L11-OTHER-ACANTHOLYTIC-DISORDERS

ICD-10-CM Code For Other Acantholytic Disorders: Group Overview

L13-OTHER-BULLOUS-DISORDERS

ICD-10-CM Code For Other Bullous Disorders: Group Overview

L14-BULLOUS-DISORDERS-IN-DISEASES-CLASSIFIED-ELSEWHERE

ICD-10-CM Code For Bullous Disorders In Diseases Classified Elsewhere: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

8 rows

ICD-10-CM Code	Description
L12.0	Bullous pemphigoid
L12.1	Cicatricial pemphigoid
L12.2	Chronic bullous disease of childhood
L12.30	Acquired epidermolysis bullosa, unspecified
L12.31	Epidermolysis bullosa due to drug
L12.35	Other acquired epidermolysis bullosa
L12.8	Other pemphigoid
L12.9	Pemphigoid, unspecified

DRG Codes

4 rows

DRG Code	Description
595	Major Skin Disorders with MCC
596	Major Skin Disorders without MCC
606	Minor Skin Disorders with MCC
607	Minor Skin Disorders without MCC

Typical Clinical Scenarios

An elderly patient presents to the emergency department with sudden onset of widespread tense blisters and pruritic urticarial plaques over the trunk and limbs, some of which have eroded and caused serous drainage; the patient reports progressive skin separation over days and mild oral mucosal involvement. The acute presentation with characteristic tense bullae and mucosal lesions prompts diagnosis and inpatient dermatology evaluation, and a bullous pemphigoid spectrum code is assigned. Typical codes: L12.0, L12.1
A middle-aged patient is seen in dermatology clinic for chronic, relapsing subepidermal blistering limited to the oral mucosa and conjunctiva, with scarring and symblepharon formation after repeated flares despite topical therapy. This represents a chronic cicatricial mucous membrane–predominant autoimmune blistering disease requiring ongoing management, and a mucous membrane–predominant pemphigoid code is used. Typical codes: L12.31, L12.35
A patient with longstanding bullous disease presents to primary care with secondary skin infection of ruptured bullae, fever, and cellulitis around multiple lesion sites; the visit documents an infectious complication of an underlying blistering disorder. Coding reflects the underlying bullous condition with notation for complications of blistering disease as applicable. Typical codes: L12.8, L12.9

Related Codes

L10-PEMPHIGUS

ICD-10-CM Code For Pemphigus: Group Overview

L11-OTHER-ACANTHOLYTIC-DISORDERS

ICD-10-CM Code For Other Acantholytic Disorders: Group Overview

L13-OTHER-BULLOUS-DISORDERS

ICD-10-CM Code For Other Bullous Disorders: Group Overview

L14-BULLOUS-DISORDERS-IN-DISEASES-CLASSIFIED-ELSEWHERE

ICD-10-CM Code For Bullous Disorders In Diseases Classified Elsewhere: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Pemphigoid: Group Overview

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ICD-10-CM L12: Pemphigoid Overview

ICD-10-CM Code For Pemphigoid: Group Overview

Sign up for ICD-10-CM Code For Pemphigoid: Group Overview policy alerts

ICD-10-CM L12: Pemphigoid Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in the ICD-10-CM L12 pemphigoid group?

How does accurate coding within L12 impact claims?

Which DRGs are related to the L12 pemphigoid group?

What clinical features should be captured when documenting an L12 diagnosis?

How are variants and causes represented within the L12 codes?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in the ICD-10-CM L12 pemphigoid group?

How does accurate coding within L12 impact claims?

Which DRGs are related to the L12 pemphigoid group?

What clinical features should be captured when documenting an L12 diagnosis?

How are variants and causes represented within the L12 codes?

References