ICD-10-CM Code For Other Acantholytic Disorders: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group L11 includes acantholytic dermatoses such as pemphigus variants and other disorders marked by intraepidermal blistering and loss of keratinocyte adhesion. These ICD-10-CM diagnosis codes are used to document clinical scenarios including mucocutaneous involvement, disease severity, and complications like secondary infection or extensive erosions. Accurate coding within the ICD-10-CM L11 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

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ICD-10-CM L11: Other Acantholytic Disorders Overview

The Other Acantholytic Disorders group includes diseases characterized by loss of cell-to-cell adhesion within the epidermis leading to blistering and erosions, often involving mucocutaneous surfaces. These conditions target the integumentary system and can reflect autoimmune, genetic, or idiopathic processes. Accurate coding matters for appropriate clinical documentation and supports correct reimbursement for dermatologic care.

When to Use

Use a code from this group when a patient has a documented diagnosis of an acantholytic blistering disorder confirmed by clinical evaluation, biopsy, or immunopathology. Select the most specific code reflecting the subtype, anatomic involvement, and any documented complications to ensure accurate documentation.

ICD-10-CM Codes

4 rows

ICD-10-CM Code	Description
L11.0	Acquired keratosis follicularis
L11.1	Transient acantholytic dermatosis [Grover]
L11.8	Other specified acantholytic disorders
L11.9	Acantholytic disorder, unspecified

DRG Codes

2 rows

DRG Code	Description
606	Minor Skin Disorders with MCC
607	Minor Skin Disorders without MCC

Typical Clinical Scenarios

An elderly patient presents to the dermatology clinic with weeks of progressive flaccid blisters and erosions on the trunk and mucous membranes, accompanied by painful oral ulcers and positive Nikolsky sign. Biopsy shows suprabasal acantholysis with IgG deposition on direct immunofluorescence, consistent with pemphigus vulgaris; a specific acantholytic bullous disorder diagnosis from this group is assigned for definitive coding and ongoing management. Typical codes: L11.0, L11.9
A middle-aged patient with a history of long-standing, relapsing superficial blisters localized to the groin and intertriginous areas presents for evaluation after topical therapy failure; skin biopsy demonstrates intraepidermal acantholysis without mucosal involvement. Because this represents a chronic, non-pemphigus acantholytic disorder manifesting with recurrent localized lesions, a code from this group is used to capture the chronic cutaneous acantholysis. Typical codes: L11.1, L11.8
A hospitalized patient develops widespread blistering and secondary bacterial infection after a drug exposure; cultures are positive and the patient requires IV antibiotics and wound care. The acute complication of an acantholytic bullous disorder with superinfection is coded using one of the group’s codes to reflect the underlying acantholytic disease contributing to the infectious complication. Typical codes: L11.8, L11.9

Related Codes

L10-PEMPHIGUS

ICD-10-CM Code For Pemphigus: Group Overview

L12-PEMPHIGOID

ICD-10-CM Code For Pemphigoid: Group Overview

L13-OTHER-BULLOUS-DISORDERS

ICD-10-CM Code For Other Bullous Disorders: Group Overview

L14-BULLOUS-DISORDERS-IN-DISEASES-CLASSIFIED-ELSEWHERE

ICD-10-CM Code For Bullous Disorders In Diseases Classified Elsewhere: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

4 rows

ICD-10-CM Code	Description
L11.0	Acquired keratosis follicularis
L11.1	Transient acantholytic dermatosis [Grover]
L11.8	Other specified acantholytic disorders
L11.9	Acantholytic disorder, unspecified

DRG Codes

2 rows

DRG Code	Description
606	Minor Skin Disorders with MCC
607	Minor Skin Disorders without MCC

Typical Clinical Scenarios

An elderly patient presents to the dermatology clinic with weeks of progressive flaccid blisters and erosions on the trunk and mucous membranes, accompanied by painful oral ulcers and positive Nikolsky sign. Biopsy shows suprabasal acantholysis with IgG deposition on direct immunofluorescence, consistent with pemphigus vulgaris; a specific acantholytic bullous disorder diagnosis from this group is assigned for definitive coding and ongoing management. Typical codes: L11.0, L11.9
A middle-aged patient with a history of long-standing, relapsing superficial blisters localized to the groin and intertriginous areas presents for evaluation after topical therapy failure; skin biopsy demonstrates intraepidermal acantholysis without mucosal involvement. Because this represents a chronic, non-pemphigus acantholytic disorder manifesting with recurrent localized lesions, a code from this group is used to capture the chronic cutaneous acantholysis. Typical codes: L11.1, L11.8
A hospitalized patient develops widespread blistering and secondary bacterial infection after a drug exposure; cultures are positive and the patient requires IV antibiotics and wound care. The acute complication of an acantholytic bullous disorder with superinfection is coded using one of the group’s codes to reflect the underlying acantholytic disease contributing to the infectious complication. Typical codes: L11.8, L11.9

Related Codes

L10-PEMPHIGUS

ICD-10-CM Code For Pemphigus: Group Overview

L12-PEMPHIGOID

ICD-10-CM Code For Pemphigoid: Group Overview

L13-OTHER-BULLOUS-DISORDERS

ICD-10-CM Code For Other Bullous Disorders: Group Overview

L14-BULLOUS-DISORDERS-IN-DISEASES-CLASSIFIED-ELSEWHERE

ICD-10-CM Code For Bullous Disorders In Diseases Classified Elsewhere: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Other Acantholytic Disorders: Group Overview

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ICD-10-CM L11: Other Acantholytic Disorders Overview

ICD-10-CM Code For Other Acantholytic Disorders: Group Overview

Sign up for ICD-10-CM Code For Other Acantholytic Disorders: Group Overview policy alerts

ICD-10-CM L11: Other Acantholytic Disorders Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in the ICD-10-CM L11 group?

How does accurate coding within the L11 group impact reimbursement?

What clinical scenarios are documented with codes from L11?

Which DRGs are related to the Other Acantholytic Disorders group?

What does the introduction say about the causes and system affected by L11 disorders?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in the ICD-10-CM L11 group?

How does accurate coding within the L11 group impact reimbursement?

What clinical scenarios are documented with codes from L11?

Which DRGs are related to the Other Acantholytic Disorders group?

What does the introduction say about the causes and system affected by L11 disorders?

References