ICD-10-CM Code For Hereditary And Idiopathic Neuropathy: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group G60 includes hereditary and idiopathic peripheral neuropathies such as Charcot-Marie-Tooth disease and other genetic or idiopathic polyneuropathies that primarily affect peripheral nerves and may present with motor, sensory, or autonomic involvement. These ICD-10-CM diagnosis codes are used to document clinical scenarios involving chronic or progressive peripheral nerve dysfunction, capturing disease distribution, severity, and any associated functional impairment. Accurate coding within the ICD-10-CM G60 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

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ICD-10-CM G60: Hereditary And Idiopathic Neuropathy Overview

The ICD-10-CM G60 group captures hereditary and idiopathic neuropathies affecting peripheral nerves, including inherited sensorimotor and sensory-only neuropathies. These conditions target the peripheral nervous system and can cause weakness, numbness, pain, and autonomic dysfunction. Accurate coding matters for reimbursement because it supports clear documentation of diagnosis etiology and guides appropriate benefit determination.

When to Use

Use a code from this group when a clinical assessment or diagnostic testing identifies a hereditary or idiopathic peripheral neuropathy as the primary diagnosis. Select the specific code to reflect the documented subtype, distribution, and any associated functional impairment or complications.

ICD-10-CM Codes

6 rows

ICD-10-CM Code	Description
G60.0	Hereditary motor and sensory neuropathy
G60.1	Refsum's disease
G60.2	Neuropathy in association with hereditary ataxia
G60.3	Idiopathic progressive neuropathy
G60.8	Other hereditary and idiopathic neuropathies
G60.9	Hereditary and idiopathic neuropathy, unspecified

DRG Codes

5 rows

DRG Code	Description
073	Cranial and Peripheral Nerve Disorders with MCC
074	Cranial and Peripheral Nerve Disorders without MCC
091	Other Disorders of Nervous System with MCC
092	Other Disorders of Nervous System with CC
093	Other Disorders of Nervous System without CC/MCC

Typical Clinical Scenarios

An adult patient in the emergency department presents with rapidly progressive symmetric distal weakness, numbness, and paresthesias over days to weeks following a gastrointestinal illness; neurologic exam shows decreased deep tendon reflexes and glove-and-stocking sensory loss, and nerve conduction studies demonstrate demyelinating polyneuropathy. The acute/subacute presentation prompting urgent evaluation and electrodiagnostic testing leads to assignment of a hereditary/idiopathic neuropathy code when no systemic cause is identified. Typical codes: G60.9, G60.8
A middle-aged patient in outpatient neurology clinic with a long-standing history of slowly progressive distal sensorimotor neuropathy, family history of similar symptoms, pes cavus, and genetic testing confirming a hereditary demyelinating neuropathy. The chronic, inherited pattern with confirmatory testing results in coding from this group to capture the hereditary neuropathy as the primary neurologic disorder. Typical codes: G60.0, G60.2
A hospitalized patient with diabetes is admitted for foot ulcer management and is found to have chronic sensory loss and motor weakness from a separate idiopathic polyneuropathy that complicates wound care and mobility; the neuropathy is not attributable to the diabetic etiology after clinical review. Coding from this group is used to document the coexisting hereditary or idiopathic peripheral neuropathy as a comorbidity affecting care. Typical codes: G60.9, G60.8

Related Codes

G61-INFLAMMATORY-POLYNEUROPATHY

ICD-10-CM Code For Inflammatory Polyneuropathy: Group Overview

G62-OTHER-AND-UNSPECIFIED-POLYNEUROPATHIES

ICD-10-CM Code For Other And Unspecified Polyneuropathies: Group Overview

G63-POLYNEUROPATHY-IN-DISEASES-CLASSIFIED-ELSEWHERE

ICD-10-CM Code For Polyneuropathy In Diseases Classified Elsewhere: Group Overview

G64-OTHER-PERIPHERAL-NERVE-DISORDERS

ICD-10-CM Code For Other Disorders Of Peripheral Nervous System: Group Overview

G65-SEQUELAE-OF-POLYNEUROPATHIES

ICD-10-CM Code For Sequelae Of Inflammatory And Toxic Polyneuropathies: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

6 rows

ICD-10-CM Code	Description
G60.0	Hereditary motor and sensory neuropathy
G60.1	Refsum's disease
G60.2	Neuropathy in association with hereditary ataxia
G60.3	Idiopathic progressive neuropathy
G60.8	Other hereditary and idiopathic neuropathies
G60.9	Hereditary and idiopathic neuropathy, unspecified

DRG Codes

5 rows

DRG Code	Description
073	Cranial and Peripheral Nerve Disorders with MCC
074	Cranial and Peripheral Nerve Disorders without MCC
091	Other Disorders of Nervous System with MCC
092	Other Disorders of Nervous System with CC
093	Other Disorders of Nervous System without CC/MCC

Typical Clinical Scenarios

An adult patient in the emergency department presents with rapidly progressive symmetric distal weakness, numbness, and paresthesias over days to weeks following a gastrointestinal illness; neurologic exam shows decreased deep tendon reflexes and glove-and-stocking sensory loss, and nerve conduction studies demonstrate demyelinating polyneuropathy. The acute/subacute presentation prompting urgent evaluation and electrodiagnostic testing leads to assignment of a hereditary/idiopathic neuropathy code when no systemic cause is identified. Typical codes: G60.9, G60.8
A middle-aged patient in outpatient neurology clinic with a long-standing history of slowly progressive distal sensorimotor neuropathy, family history of similar symptoms, pes cavus, and genetic testing confirming a hereditary demyelinating neuropathy. The chronic, inherited pattern with confirmatory testing results in coding from this group to capture the hereditary neuropathy as the primary neurologic disorder. Typical codes: G60.0, G60.2
A hospitalized patient with diabetes is admitted for foot ulcer management and is found to have chronic sensory loss and motor weakness from a separate idiopathic polyneuropathy that complicates wound care and mobility; the neuropathy is not attributable to the diabetic etiology after clinical review. Coding from this group is used to document the coexisting hereditary or idiopathic peripheral neuropathy as a comorbidity affecting care. Typical codes: G60.9, G60.8

Related Codes

G61-INFLAMMATORY-POLYNEUROPATHY

ICD-10-CM Code For Inflammatory Polyneuropathy: Group Overview

G62-OTHER-AND-UNSPECIFIED-POLYNEUROPATHIES

ICD-10-CM Code For Other And Unspecified Polyneuropathies: Group Overview

G63-POLYNEUROPATHY-IN-DISEASES-CLASSIFIED-ELSEWHERE

ICD-10-CM Code For Polyneuropathy In Diseases Classified Elsewhere: Group Overview

G64-OTHER-PERIPHERAL-NERVE-DISORDERS

ICD-10-CM Code For Other Disorders Of Peripheral Nervous System: Group Overview

G65-SEQUELAE-OF-POLYNEUROPATHIES

ICD-10-CM Code For Sequelae Of Inflammatory And Toxic Polyneuropathies: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Hereditary And Idiopathic Neuropathy: Group Overview

Sign up for ICD-10-CM Code For Hereditary And Idiopathic Neuropathy: Group Overview policy alerts

ICD-10-CM G60: Hereditary And Idiopathic Neuropathy Overview

ICD-10-CM Code For Hereditary And Idiopathic Neuropathy: Group Overview

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ICD-10-CM G60: Hereditary And Idiopathic Neuropathy Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in the ICD-10-CM G60 group?

How does accurate coding in the `G60` group affect reimbursement?

What specific `G60` codes should be used for hereditary motor and sensory neuropathy and unspecified cases?

Which DRGs are related to conditions coded in the G60 group?

What clinical features are captured by G60 diagnoses that coders should document?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in the ICD-10-CM G60 group?

How does accurate coding in the `G60` group affect reimbursement?

What specific `G60` codes should be used for hereditary motor and sensory neuropathy and unspecified cases?

Which DRGs are related to conditions coded in the G60 group?

What clinical features are captured by G60 diagnoses that coders should document?

References