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    OpenPayerBilling CodesSystemic atrophies primarily affecting the central nervous systemICD-10-CM g13-systemic-atrophies-central-nervous-system
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    ICD-10-CM Code For Systemic Atrophies Primarily Affecting Central Nervous System: Group Overview

    The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group G13 includes systemic atrophies that primarily affect the central nervous system when those atrophies are manifestations of diseases classified elsewhere, such as metabolic, infectious, or inflammatory disorders. These ICD-10-CM diagnosis codes are used to document central nervous system degeneration that is secondary to another underlying disease, capturing the relationship between the neurologic findings and the primary condition. Accurate coding within the ICD-10-CM G13 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

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    ICD-10-CM G13: Systemic Atrophies Primarily Affecting Central Nervous System In Diseases Classified Elsewhere Overview

    This group represents systemic atrophies that primarily affect the central nervous system but occur in the context of other diseases classified elsewhere. It targets neurodegenerative changes and central nervous system involvement secondary to systemic conditions. Accurate coding matters because it links the neurological manifestation to the underlying condition for correct clinical documentation and reimbursement.

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    When to Use

    Use codes from this group when documenting central nervous system atrophy that is explicitly attributed to another disease documented elsewhere in the record. These codes should be used to reflect the neurologic manifestation in conjunction with the code for the underlying condition.

    ICD-10-CM Codes

    4 rows

    ICD-10-CM CodeDescription
    G13.0Paraneoplastic neuromyopathy and neuropathy
    G13.1Other systemic atrophy primarily affecting central nervous system in neoplastic disease
    G13.2Systemic atrophy primarily affecting the central nervous system in myxedema
    G13.8Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere

    DRG Codes

    4 rows

    DRG CodeDescription
    056Degenerative Nervous System Disorders with MCC
    057Degenerative Nervous System Disorders without MCC
    073Cranial and Peripheral Nerve Disorders with MCC
    074Cranial and Peripheral Nerve Disorders without MCC

    Typical Clinical Scenarios

    • A middle-aged adult with long-standing myasthenia gravis controlled on immunosuppression develops progressive generalized muscle wasting, bulbar weakness, and increasing respiratory compromise over months; the patient presents for evaluation of worsening neuromuscular atrophy and functional decline after failure of multiple therapies. A diagnosis from this group is assigned because the primary process is a systemic neuromuscular disease causing predominant central nervous system-related atrophy and functional deterioration. Typical codes: G13.0, G13.8
    • An elderly patient with documented multisystem autoimmune disease (such as systemic lupus erythematosus) develops progressive cerebellar ataxia, gait instability, and cognitive slowing over several months prompting neurology referral and imaging to evaluate for neurodegenerative involvement related to the systemic illness. A code in this group is used when a systemic disease primarily affects the central nervous system with atrophic changes and neurologic decline as a complication of the underlying disorder. Typical codes: G13.1, G13.8
    • A younger adult presents to the emergency department after an acute exacerbation of a metabolic storage disorder with new onset rapid motor decline, spasticity, and diffuse central nervous system atrophy documented on MRI; the hospitalization focuses on stabilization and diagnostic workup of the systemic disease causing CNS degeneration. This group’s diagnosis is applied when systemic metabolic or storage diseases primarily produce central nervous system atrophy requiring inpatient management for acute deterioration. Typical codes: G13.2, G13.8

    Related Codes

    G10-HUNTINGTON-S-DISEASE

    ICD-10-CM Code For Huntington's Disease: Group Overview

    G11-HEREDITARY-ATAXIA

    ICD-10-CM Code For Hereditary Ataxia: Group Overview

    G12-SPINAL-MUSCULAR-ATROPHY-AND-RELATED-SYNDROMES

    ICD-10-CM Code For Spinal Muscular Atrophy And Related Syndromes: Group Overview

    G14-POSTPOLIO-SYNDROME

    ICD-10-CM Code For Postpolio Syndrome: Group Overview

    Frequently Asked Questions

    References

    1. 1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
    2. 2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
    3. 3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.
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