ICD-10-CM Code For Huntington's Disease: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group G10 includes Huntington's disease and related inherited chorea conditions characterized by progressive movement disorder, cognitive decline, and psychiatric symptoms. These ICD-10-CM diagnosis codes are used to document clinical presentations of hereditary neurodegeneration, capturing disease severity, neurologic system involvement, and associated psychiatric or cognitive complications relevant to this group. Accurate coding within the ICD-10-CM G10 group supports proper claim adjudication / complete clinical documentation / appropriate reimbursement.

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ICD-10-CM G10: Huntington's Disease Overview

The ICD-10-CM G10 group contains diagnoses for Huntington's disease, a progressive neurodegenerative disorder affecting the central nervous system. These codes represent inherited chorea, cognitive decline, and psychiatric manifestations that primarily involve the basal ganglia and related neural circuits. Accurate coding is important to reflect disease severity and neurologic complications, which supports appropriate reimbursement and continuity of care.

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ICD-10-CM Code For Huntington's Disease: Group Overview

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ICD-10-CM G10: Huntington's Disease Overview

When to Use

Use a code from this group when Huntington's disease has been clinically diagnosed or documented by a qualified clinician and is relevant to the current encounter. Apply these codes to capture disease manifestations, progression, and any complications that affect treatment, care planning, or claim submission.

ICD-10-CM Codes

1 rows

ICD-10-CM Code	Description
G10	Huntington's disease

DRG Codes

2 rows

DRG Code	Description
056	Degenerative Nervous System Disorders with MCC
057	Degenerative Nervous System Disorders without MCC

Typical Clinical Scenarios

A middle-aged adult presents to neurology clinic with a several-year history of progressive involuntary choreic movements, cognitive decline with executive dysfunction, and psychiatric symptoms including irritability and depression; family history is positive for a similar disorder and genetic testing confirms an expanded CAG repeat. The patient is seen for routine management of the neurodegenerative disorder and documentation of baseline motor and cognitive status prior to symptomatic therapy adjustments. Typical codes: G10
An older patient arrives at the emergency department after a fall related to abrupt worsening of balance and chorea, with new onset dysphagia and aspiration risk; inpatient evaluation includes airway and swallowing assessment and initiation of inpatient supportive care. The acute presentation and known underlying neurodegenerative movement disorder lead to assignment of a code from this group as the primary neurologic diagnosis complicating the acute event. Typical codes: G10
A young adult with a known hereditary neurodegenerative movement disorder is admitted to an inpatient psychiatric unit for severe depression with suicidal ideation that is believed to be related to progression of the underlying disease; multidisciplinary care addresses psychiatric stabilization and coordination with neurology for ongoing management. The chronic central nervous system condition is coded to reflect the underlying disease contributing to psychiatric comorbidity and care complexity. Typical codes: G10

Related Codes

G11-HEREDITARY-ATAXIA

ICD-10-CM Code For Hereditary Ataxia: Group Overview

G12-SPINAL-MUSCULAR-ATROPHY-AND-RELATED-SYNDROMES

ICD-10-CM Code For Spinal Muscular Atrophy And Related Syndromes: Group Overview

G13-SYSTEMIC-ATROPHIES-CENTRAL-NERVOUS-SYSTEM

ICD-10-CM Code For Systemic Atrophies Primarily Affecting Central Nervous System: Group Overview

G14-POSTPOLIO-SYNDROME

ICD-10-CM Code For Postpolio Syndrome: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

1 rows

ICD-10-CM Code	Description
G10	Huntington's disease

DRG Codes

2 rows

DRG Code	Description
056	Degenerative Nervous System Disorders with MCC
057	Degenerative Nervous System Disorders without MCC

Typical Clinical Scenarios

A middle-aged adult presents to neurology clinic with a several-year history of progressive involuntary choreic movements, cognitive decline with executive dysfunction, and psychiatric symptoms including irritability and depression; family history is positive for a similar disorder and genetic testing confirms an expanded CAG repeat. The patient is seen for routine management of the neurodegenerative disorder and documentation of baseline motor and cognitive status prior to symptomatic therapy adjustments. Typical codes: G10
An older patient arrives at the emergency department after a fall related to abrupt worsening of balance and chorea, with new onset dysphagia and aspiration risk; inpatient evaluation includes airway and swallowing assessment and initiation of inpatient supportive care. The acute presentation and known underlying neurodegenerative movement disorder lead to assignment of a code from this group as the primary neurologic diagnosis complicating the acute event. Typical codes: G10
A young adult with a known hereditary neurodegenerative movement disorder is admitted to an inpatient psychiatric unit for severe depression with suicidal ideation that is believed to be related to progression of the underlying disease; multidisciplinary care addresses psychiatric stabilization and coordination with neurology for ongoing management. The chronic central nervous system condition is coded to reflect the underlying disease contributing to psychiatric comorbidity and care complexity. Typical codes: G10

Related Codes

G11-HEREDITARY-ATAXIA

ICD-10-CM Code For Hereditary Ataxia: Group Overview

G12-SPINAL-MUSCULAR-ATROPHY-AND-RELATED-SYNDROMES

ICD-10-CM Code For Spinal Muscular Atrophy And Related Syndromes: Group Overview

G13-SYSTEMIC-ATROPHIES-CENTRAL-NERVOUS-SYSTEM

ICD-10-CM Code For Systemic Atrophies Primarily Affecting Central Nervous System: Group Overview

G14-POSTPOLIO-SYNDROME

ICD-10-CM Code For Postpolio Syndrome: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Huntington's Disease: Group Overview

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ICD-10-CM G10: Huntington's Disease Overview

ICD-10-CM Code For Huntington's Disease: Group Overview

Sign up for ICD-10-CM Code For Huntington's Disease: Group Overview policy alerts

ICD-10-CM G10: Huntington's Disease Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which diagnosis does the ICD-10-CM G10 group represent?

How do codes in the `G10` group support reimbursement and billing?

What clinical features are documented by `ICD-10-CM` `G10` codes?

Which DRGs are related to the `G10` Huntington's disease group?

Why is accurate documentation important for `ICD-10-CM` `G10` coding?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which diagnosis does the ICD-10-CM G10 group represent?

How do codes in the `G10` group support reimbursement and billing?

What clinical features are documented by `ICD-10-CM` `G10` codes?

Which DRGs are related to the `G10` Huntington's disease group?

Why is accurate documentation important for `ICD-10-CM` `G10` coding?

References