ICD-10-CM Code For Other Congenital Malformations Of Urinary System: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group Q64 includes congenital malformations of the urinary system such as renal hypoplasia, renal dysplasia, ectopic kidney, duplication anomalies, and other specified congenital anomalies of the kidneys, ureters, and bladder. These ICD-10-CM diagnosis codes are used to document congenital structural abnormalities of urinary organs, capturing anatomic details, laterality, and any associated functional impairment important for clinical records. Accurate coding within the ICD-10-CM Q64 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

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ICD-10-CM Q64: Other Congenital Malformations Of Urinary System Overview

The ICD-10-CM Q64 code group covers congenital structural anomalies of the urinary tract that are not classified elsewhere. These diagnoses target malformations of kidneys, ureters, bladder, and related urinary structures present at birth. Accurate coding supports appropriate claim processing and reflects clinical complexity relevant to care and resource use.

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ICD-10-CM Code For Other Congenital Malformations Of Urinary System: Group Overview

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ICD-10-CM Q64: Other Congenital Malformations Of Urinary System Overview

When to Use

Assign a code from this group when a congenital structural anomaly of the urinary tract is the documented diagnosis and pertains to clinical care, evaluation, or billing. Use the most specific code available to reflect the anatomic site, laterality, and any noted functional impairment.

ICD-10-CM Codes

22 rows

ICD-10-CM Code	Description
Q64.0	Epispadias
Q64.10	Exstrophy of urinary bladder, unspecified
Q64.11	Supravesical fissure of urinary bladder
Q64.12	Cloacal exstrophy of urinary bladder
Q64.19	Other exstrophy of urinary bladder
Q64.2	Congenital posterior urethral valves
Q64.31	Congenital bladder neck obstruction
Q64.32	Congenital stricture of urethra
Q64.33	Congenital stricture of urinary meatus
Q64.39	Other atresia and stenosis of urethra and bladder neck
Q64.4	Malformation of urachus
Q64.5	Congenital absence of bladder and urethra
Q64.6	Congenital diverticulum of bladder
Q64.70	Unspecified congenital malformation of bladder and urethra
Q64.71	Congenital prolapse of urethra
Q64.72	Congenital prolapse of urinary meatus
Q64.73	Congenital urethrorectal fistula
Q64.74	Double urethra
Q64.75	Double urinary meatus
Q64.79	Other congenital malformations of bladder and urethra

Showing 1–20 of 22

DRG Codes

5 rows

DRG Code	Description
698	Other Kidney and Urinary Tract Diagnoses with MCC
699	Other Kidney and Urinary Tract Diagnoses with CC
700	Other Kidney and Urinary Tract Diagnoses without CC/MCC
729	Other Male Reproductive System Diagnoses with CC/MCC
730	Other Male Reproductive System Diagnoses without CC/MCC

Typical Clinical Scenarios

A newborn male is noted on newborn exam and prenatal ultrasound to have an abdominal mass and poor urine output; postnatal ultrasound demonstrates hydronephrosis and a unilateral duplicated renal pelvis with duplex collecting system leading to recurrent urinary stasis. The infant is referred to pediatric urology for evaluation of obstruction and possible surgical correction; a congenital anomaly of the renal collecting system is assigned to describe the structural duplication. Typical codes: Q64.31, Q64.32, Q64.33
A school-age child with a history of recurrent urinary tract infections and daytime urinary incontinence undergoes voiding cystourethrogram and renal ultrasound showing vesicoureteral reflux associated with congenital posterior urethral valves and bladder diverticulum. The child presents for outpatient evaluation and long-term management of the anatomic cause of recurrent infections and bladder dysfunction; a congenital malformation of the bladder outlet or urethra is coded to capture the underlying congenital abnormality. Typical codes: Q64.10, Q64.11, Q64.12
An adult presents to the emergency department with acute flank pain and sepsis from obstructive pyelonephritis; imaging reveals a single ectopic kidney with severe hydronephrosis and stone formation causing urinary obstruction. The congenital positional anomaly of the kidney is documented as the underlying condition contributing to the acute complication and guides both acute management and future urologic planning. Typical codes: Q64.4, Q64.5

ICD-10-CM Code For Renal Agenesis And Other Reduction Defects Of Kidney: Group Overview

Q61-CYSTIC-KIDNEY-DISEASE

ICD-10-CM Code For Cystic Kidney Disease: Group Overview

Q62-CONGENITAL-OBSTRUCTIVE-DEFECTS-RENAL-PELVIS-URETER

ICD-10-CM Code For Congenital Obstructive Defects Of Renal Pelvis And Congenital Malformations Of Ureter: Group Overview

Q63-OTHER-CONGENITAL-MALFORMATIONS-OF-KIDNEY

ICD-10-CM Code For Other Congenital Malformations Of Kidney: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

22 rows

ICD-10-CM Code	Description
Q64.0	Epispadias
Q64.10	Exstrophy of urinary bladder, unspecified
Q64.11	Supravesical fissure of urinary bladder
Q64.12	Cloacal exstrophy of urinary bladder
Q64.19	Other exstrophy of urinary bladder
Q64.2	Congenital posterior urethral valves
Q64.31	Congenital bladder neck obstruction
Q64.32	Congenital stricture of urethra
Q64.33	Congenital stricture of urinary meatus
Q64.39	Other atresia and stenosis of urethra and bladder neck
Q64.4	Malformation of urachus
Q64.5	Congenital absence of bladder and urethra
Q64.6	Congenital diverticulum of bladder
Q64.70	Unspecified congenital malformation of bladder and urethra
Q64.71	Congenital prolapse of urethra
Q64.72	Congenital prolapse of urinary meatus
Q64.73	Congenital urethrorectal fistula
Q64.74	Double urethra
Q64.75	Double urinary meatus
Q64.79	Other congenital malformations of bladder and urethra

Showing 1–20 of 22

DRG Codes

5 rows

DRG Code	Description
698	Other Kidney and Urinary Tract Diagnoses with MCC
699	Other Kidney and Urinary Tract Diagnoses with CC
700	Other Kidney and Urinary Tract Diagnoses without CC/MCC
729	Other Male Reproductive System Diagnoses with CC/MCC
730	Other Male Reproductive System Diagnoses without CC/MCC

Typical Clinical Scenarios

A newborn male is noted on newborn exam and prenatal ultrasound to have an abdominal mass and poor urine output; postnatal ultrasound demonstrates hydronephrosis and a unilateral duplicated renal pelvis with duplex collecting system leading to recurrent urinary stasis. The infant is referred to pediatric urology for evaluation of obstruction and possible surgical correction; a congenital anomaly of the renal collecting system is assigned to describe the structural duplication. Typical codes: Q64.31, Q64.32, Q64.33
A school-age child with a history of recurrent urinary tract infections and daytime urinary incontinence undergoes voiding cystourethrogram and renal ultrasound showing vesicoureteral reflux associated with congenital posterior urethral valves and bladder diverticulum. The child presents for outpatient evaluation and long-term management of the anatomic cause of recurrent infections and bladder dysfunction; a congenital malformation of the bladder outlet or urethra is coded to capture the underlying congenital abnormality. Typical codes: Q64.10, Q64.11, Q64.12
An adult presents to the emergency department with acute flank pain and sepsis from obstructive pyelonephritis; imaging reveals a single ectopic kidney with severe hydronephrosis and stone formation causing urinary obstruction. The congenital positional anomaly of the kidney is documented as the underlying condition contributing to the acute complication and guides both acute management and future urologic planning. Typical codes: Q64.4, Q64.5

ICD-10-CM Code For Renal Agenesis And Other Reduction Defects Of Kidney: Group Overview

Q61-CYSTIC-KIDNEY-DISEASE

ICD-10-CM Code For Cystic Kidney Disease: Group Overview

Q62-CONGENITAL-OBSTRUCTIVE-DEFECTS-RENAL-PELVIS-URETER

ICD-10-CM Code For Congenital Obstructive Defects Of Renal Pelvis And Congenital Malformations Of Ureter: Group Overview

Q63-OTHER-CONGENITAL-MALFORMATIONS-OF-KIDNEY

ICD-10-CM Code For Other Congenital Malformations Of Kidney: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

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ICD-10-CM Code For Other Congenital Malformations Of Urinary System: Group Overview

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ICD-10-CM Q64: Other Congenital Malformations Of Urinary System Overview

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ICD-10-CM Q64: Other Congenital Malformations Of Urinary System Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

References

ICD-10-CM Code For Other Congenital Malformations Of Urinary System: Group Overview

Sign up for ICD-10-CM Code For Other Congenital Malformations Of Urinary System: Group Overview policy alerts

ICD-10-CM Q64: Other Congenital Malformations Of Urinary System Overview

ICD-10-CM Code For Other Congenital Malformations Of Urinary System: Group Overview

Sign up for ICD-10-CM Code For Other Congenital Malformations Of Urinary System: Group Overview policy alerts

ICD-10-CM Q64: Other Congenital Malformations Of Urinary System Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in the ICD-10-CM Q64 group?

How should coders capture laterality or anatomic detail for Q64 diagnoses?

Which DRGs may be related to claims with Q64 codes?

Are there specific Q64 codes for bladder exstrophy variants?

What documentation goals should clinicians and coders focus on for Q64 group entries?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in the ICD-10-CM Q64 group?

How should coders capture laterality or anatomic detail for Q64 diagnoses?

Which DRGs may be related to claims with Q64 codes?

Are there specific Q64 codes for bladder exstrophy variants?

What documentation goals should clinicians and coders focus on for Q64 group entries?

References