ICD-10-CM Code For Indeterminate Sex And Pseudohermaphroditism: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group Q56 includes congenital conditions characterized by indeterminate sex and pseudohermaphroditism, covering disorders of sexual development and atypical genital formation. These ICD-10-CM diagnosis codes are used to document congenital genital organ malformations, capture anatomical and developmental involvement, and note clinical complexity in newborns and pediatric patients. Accurate coding within the ICD-10-CM Q56 group supports proper claim adjudication and complete clinical documentation for appropriate reimbursement.

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ICD-10-CM Q56: Indeterminate Sex And Pseudohermaphroditism Overview

This group captures congenital conditions where chromosomal, gonadal, or phenotypic sex is ambiguous or where external genitalia do not match typical male or female development. It targets congenital malformations of the genital organs and disorders of sexual development present at birth. Accurate coding is important for clinical documentation and impacts coding-based reimbursement and resource allocation.

When to Use

Use a code from this group when documenting a newborn or pediatric patient with ambiguous genitalia, disorders of sex development, or identified pseudohermaphroditism based on clinical assessment and diagnostic findings. Codes in this group are appropriate when the primary clinical concern is congenital atypical development of the genital organs requiring classification for care, monitoring, or administrative purposes.

ICD-10-CM Codes

5 rows

ICD-10-CM Code	Description
Q56.0	Hermaphroditism, not elsewhere classified
Q56.1	Male pseudohermaphroditism, not elsewhere classified
Q56.2	Female pseudohermaphroditism, not elsewhere classified
Q56.3	Pseudohermaphroditism, unspecified
Q56.4	Indeterminate sex, unspecified

DRG Codes

6 rows

DRG Code	Description
729	Other Male Reproductive System Diagnoses with CC/MCC
730	Other Male Reproductive System Diagnoses without CC/MCC
742	Uterine and Adnexa Procedures for Non-Malignancy with CC/MCC
743	Uterine and Adnexa Procedures for Non-Malignancy without CC/MCC
760	Menstrual and Other Female Reproductive System Disorders with CC/MCC
761	Menstrual and Other Female Reproductive System Disorders without CC/MCC

Typical Clinical Scenarios

A newborn with ambiguous external genitalia is evaluated in the neonatal unit after delivery; the infant presents with atypical genital morphology and unclear sex assignment on physical exam, prompting endocrine, genetic, and urologic assessment to determine underlying disorder of sex development. A congenital malformation code from this group is assigned to document indeterminate sex/pseudohermaphroditism as part of the diagnostic workup and initial problem list. Typical codes: Q56.0, Q56.1
An adolescent assigned female at birth presents to pediatric endocrinology for primary amenorrhea and virilization with clitoromegaly and ambiguous genital features identified on prior childhood records; evaluation includes karyotype and hormone studies to characterize a congenital intersex condition established earlier but newly being managed for pubertal development. A code from this group is used to capture the congenital pseudohermaphroditism/indeterminate sex as the underlying diagnosis guiding long-term endocrine and surgical planning. Typical codes: Q56.2, Q56.3
An adult with a known congenital intersex condition is admitted for reconstructive genital surgery due to urinary obstruction and recurrent infections related to atypical urethral anatomy; perioperative documentation requires coding of the congenital genital malformation as a comorbidity contributing to the current complication and surgical approach. A code from this group is recorded to reflect the structural congenital anomaly influencing treatment and postoperative care. Typical codes: Q56.4, Q56.1}

Related Codes

Q50-CONGENITAL-MALFORMATIONS-OF-OVARIES

ICD-10-CM Code For Congenital Malformations Of Ovaries Fallopian Tubes And Broad Ligaments: Group Overview

Q51-CONGENITAL-MALFORMATIONS-OF-UTERUS-AND-CERVIX

ICD-10-CM Code For Congenital Malformations Of Uterus And Cervix: Group Overview

Q52-OTHER-CONGENITAL-MALFORMATIONS-FEMALE-GENITALIA

ICD-10-CM Code For Other Congenital Malformations Of Female Genitalia: Group Overview

Q53-UNDESCENDED-AND-ECTOPIC-TESTICLE

ICD-10-CM Code For Undescended And Ectopic Testicle: Group Overview

Q54-HYPOSPADIAS

ICD-10-CM Code For Hypospadias: Group Overview

Q55-OTHER-CONGENITAL-MALE-GENITAL-MALFORMATIONS

ICD-10-CM Code For Other Congenital Malformations Of Male Genital Organs: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

5 rows

ICD-10-CM Code	Description
Q56.0	Hermaphroditism, not elsewhere classified
Q56.1	Male pseudohermaphroditism, not elsewhere classified
Q56.2	Female pseudohermaphroditism, not elsewhere classified
Q56.3	Pseudohermaphroditism, unspecified
Q56.4	Indeterminate sex, unspecified

DRG Codes

6 rows

DRG Code	Description
729	Other Male Reproductive System Diagnoses with CC/MCC
730	Other Male Reproductive System Diagnoses without CC/MCC
742	Uterine and Adnexa Procedures for Non-Malignancy with CC/MCC
743	Uterine and Adnexa Procedures for Non-Malignancy without CC/MCC
760	Menstrual and Other Female Reproductive System Disorders with CC/MCC
761	Menstrual and Other Female Reproductive System Disorders without CC/MCC

Typical Clinical Scenarios

A newborn with ambiguous external genitalia is evaluated in the neonatal unit after delivery; the infant presents with atypical genital morphology and unclear sex assignment on physical exam, prompting endocrine, genetic, and urologic assessment to determine underlying disorder of sex development. A congenital malformation code from this group is assigned to document indeterminate sex/pseudohermaphroditism as part of the diagnostic workup and initial problem list. Typical codes: Q56.0, Q56.1
An adolescent assigned female at birth presents to pediatric endocrinology for primary amenorrhea and virilization with clitoromegaly and ambiguous genital features identified on prior childhood records; evaluation includes karyotype and hormone studies to characterize a congenital intersex condition established earlier but newly being managed for pubertal development. A code from this group is used to capture the congenital pseudohermaphroditism/indeterminate sex as the underlying diagnosis guiding long-term endocrine and surgical planning. Typical codes: Q56.2, Q56.3
An adult with a known congenital intersex condition is admitted for reconstructive genital surgery due to urinary obstruction and recurrent infections related to atypical urethral anatomy; perioperative documentation requires coding of the congenital genital malformation as a comorbidity contributing to the current complication and surgical approach. A code from this group is recorded to reflect the structural congenital anomaly influencing treatment and postoperative care. Typical codes: Q56.4, Q56.1}

Related Codes

Q50-CONGENITAL-MALFORMATIONS-OF-OVARIES

ICD-10-CM Code For Congenital Malformations Of Ovaries Fallopian Tubes And Broad Ligaments: Group Overview

Q51-CONGENITAL-MALFORMATIONS-OF-UTERUS-AND-CERVIX

ICD-10-CM Code For Congenital Malformations Of Uterus And Cervix: Group Overview

Q52-OTHER-CONGENITAL-MALFORMATIONS-FEMALE-GENITALIA

ICD-10-CM Code For Other Congenital Malformations Of Female Genitalia: Group Overview

Q53-UNDESCENDED-AND-ECTOPIC-TESTICLE

ICD-10-CM Code For Undescended And Ectopic Testicle: Group Overview

Q54-HYPOSPADIAS

ICD-10-CM Code For Hypospadias: Group Overview

Q55-OTHER-CONGENITAL-MALE-GENITAL-MALFORMATIONS

ICD-10-CM Code For Other Congenital Malformations Of Male Genital Organs: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Indeterminate Sex And Pseudohermaphroditism: Group Overview

Sign up for ICD-10-CM Code For Indeterminate Sex And Pseudohermaphroditism: Group Overview policy alerts

ICD-10-CM Q56: Indeterminate Sex And Pseudohermaphroditism Overview

ICD-10-CM Code For Indeterminate Sex And Pseudohermaphroditism: Group Overview

Sign up for ICD-10-CM Code For Indeterminate Sex And Pseudohermaphroditism: Group Overview policy alerts

ICD-10-CM Q56: Indeterminate Sex And Pseudohermaphroditism Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in ICD-10-CM code group Q56?

What specific ICD-10-CM codes are listed under the Q56 group?

How does accurate coding in the Q56 group affect reimbursement and documentation?

Which DRGs are related to ICD-10-CM Q56 diagnoses?

What patient populations are primarily captured by the Q56 code group?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in ICD-10-CM code group Q56?

What specific ICD-10-CM codes are listed under the Q56 group?

How does accurate coding in the Q56 group affect reimbursement and documentation?

Which DRGs are related to ICD-10-CM Q56 diagnoses?

What patient populations are primarily captured by the Q56 code group?

References