ICD-10-CM Code For Congenital Malformations Of Pulmonary And Tricuspid Valves: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group Q22 includes congenital malformations of the pulmonary valve and the tricuspid valve, such as pulmonary valve stenosis, pulmonary valve atresia, tricuspid atresia, and other structural anomalies present at birth. These ICD-10-CM diagnosis codes are used to document congenital valvular anomalies, capturing details such as valve structure, presence of stenosis or atresia, and associated cardiac involvement. Accurate coding within the ICD-10-CM Q22 group supports proper claim adjudication and complete clinical documentation for appropriate reimbursement.

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ICD-10-CM Q22: Congenital Malformations Of Pulmonary And Tricuspid Valves Overview

This group represents congenital malformations affecting the pulmonary valve and the tricuspid valve of the heart, conditions present from birth that can impair valvular function and cardiac hemodynamics. These diagnoses target the cardiovascular system and commonly require precise clinical description of valve morphology and severity. Accurate coding matters for complete clinical records and appropriate reimbursement determination.

When to Use

Use a code from this group when documenting a congenital malformation of the pulmonary valve or the tricuspid valve confirmed by clinical assessment, imaging, or surgical findings. Select the code that best describes the specific valve involved and the type of anomaly, such as stenosis or atresia, to reflect clinical complexity.

ICD-10-CM Codes

9 rows

ICD-10-CM Code	Description
Q22.0	Pulmonary valve atresia
Q22.1	Congenital pulmonary valve stenosis
Q22.2	Congenital pulmonary valve insufficiency
Q22.3	Other congenital malformations of pulmonary valve
Q22.4	Congenital tricuspid stenosis
Q22.5	Ebstein's anomaly
Q22.6	Hypoplastic right heart syndrome
Q22.8	Other congenital malformations of tricuspid valve
Q22.9	Congenital malformation of tricuspid valve, unspecified

DRG Codes

2 rows

DRG Code	Description
306	Cardiac Congenital and Valvular Disorders with MCC
307	Cardiac Congenital and Valvular Disorders without MCC

Typical Clinical Scenarios

A neonate born with cyanosis and a loud systolic murmur is evaluated in the newborn nursery after oxygen saturation remains low despite supplemental oxygen; echocardiography reveals an underdeveloped pulmonary valve with significant stenosis causing right ventricular hypertrophy and outflow obstruction, prompting cardiology consultation and planned balloon valvuloplasty. Typical codes: Q22.1, Q22.0
A young adult with a history of congenital heart disease presents for routine cardiology follow-up for chronic tricuspid valve regurgitation first documented in childhood; imaging and exam show progressive right-sided volume overload and symptoms of exertional dyspnea, leading to continued surveillance and consideration of valve repair. Typical codes: Q22.5, Q22.6
An infant admitted to the pediatric intensive care unit for heart failure and failure to thrive is found on echocardiogram to have complex congenital malformations including pulmonary valve atresia with ventricular septal defect and abnormal tricuspid valve anatomy contributing to hemodynamic instability; the diagnosis guides urgent multidisciplinary management and surgical planning. Typical codes: Q22.2, Q22.3, Q22.4

ICD-10-CM Code For Congenital Malformations Of Cardiac Chambers And Connections: Group Overview

Q21-CONGENITAL-CARDIAC-SEPTAL-DEFECTS

ICD-10-CM Code For Congenital Malformations Of Cardiac Septa: Group Overview

Q23-CONGENITAL-AORTIC-AND-MITRAL-VALVE-MALFORMATIONS

ICD-10-CM Code For Congenital Malformations Of Aortic And Mitral Valves: Group Overview

Q24-OTHER-CONGENITAL-MALFORMATIONS-OF-HEART

ICD-10-CM Code For Other Congenital Malformations Of Heart: Group Overview

Q25-CONGENITAL-MALFORMATIONS-OF-GREAT-ARTERIES

ICD-10-CM Code For Congenital Malformations Of Great Arteries: Group Overview

Q26-CONGENITAL-MALFORMATIONS-GREAT-VEINS

ICD-10-CM Code For Congenital Malformations Of Great Veins: Group Overview

Q27-OTHER-CONGENITAL-PERIPHERAL-VASCULAR-MALFORMATIONS

ICD-10-CM Code For Other Congenital Malformations Of Peripheral Vascular System: Group Overview

Q28-OTHER-CONGENITAL-CIRCULATORY-MALFORMATIONS

ICD-10-CM Code For Other Congenital Malformations Of Circulatory System: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

9 rows

ICD-10-CM Code	Description
Q22.0	Pulmonary valve atresia
Q22.1	Congenital pulmonary valve stenosis
Q22.2	Congenital pulmonary valve insufficiency
Q22.3	Other congenital malformations of pulmonary valve
Q22.4	Congenital tricuspid stenosis
Q22.5	Ebstein's anomaly
Q22.6	Hypoplastic right heart syndrome
Q22.8	Other congenital malformations of tricuspid valve
Q22.9	Congenital malformation of tricuspid valve, unspecified

DRG Codes

2 rows

DRG Code	Description
306	Cardiac Congenital and Valvular Disorders with MCC
307	Cardiac Congenital and Valvular Disorders without MCC

Typical Clinical Scenarios

A neonate born with cyanosis and a loud systolic murmur is evaluated in the newborn nursery after oxygen saturation remains low despite supplemental oxygen; echocardiography reveals an underdeveloped pulmonary valve with significant stenosis causing right ventricular hypertrophy and outflow obstruction, prompting cardiology consultation and planned balloon valvuloplasty. Typical codes: Q22.1, Q22.0
A young adult with a history of congenital heart disease presents for routine cardiology follow-up for chronic tricuspid valve regurgitation first documented in childhood; imaging and exam show progressive right-sided volume overload and symptoms of exertional dyspnea, leading to continued surveillance and consideration of valve repair. Typical codes: Q22.5, Q22.6
An infant admitted to the pediatric intensive care unit for heart failure and failure to thrive is found on echocardiogram to have complex congenital malformations including pulmonary valve atresia with ventricular septal defect and abnormal tricuspid valve anatomy contributing to hemodynamic instability; the diagnosis guides urgent multidisciplinary management and surgical planning. Typical codes: Q22.2, Q22.3, Q22.4

ICD-10-CM Code For Congenital Malformations Of Cardiac Chambers And Connections: Group Overview

Q21-CONGENITAL-CARDIAC-SEPTAL-DEFECTS

ICD-10-CM Code For Congenital Malformations Of Cardiac Septa: Group Overview

Q23-CONGENITAL-AORTIC-AND-MITRAL-VALVE-MALFORMATIONS

ICD-10-CM Code For Congenital Malformations Of Aortic And Mitral Valves: Group Overview

Q24-OTHER-CONGENITAL-MALFORMATIONS-OF-HEART

ICD-10-CM Code For Other Congenital Malformations Of Heart: Group Overview

Q25-CONGENITAL-MALFORMATIONS-OF-GREAT-ARTERIES

ICD-10-CM Code For Congenital Malformations Of Great Arteries: Group Overview

Q26-CONGENITAL-MALFORMATIONS-GREAT-VEINS

ICD-10-CM Code For Congenital Malformations Of Great Veins: Group Overview

Q27-OTHER-CONGENITAL-PERIPHERAL-VASCULAR-MALFORMATIONS

ICD-10-CM Code For Other Congenital Malformations Of Peripheral Vascular System: Group Overview

Q28-OTHER-CONGENITAL-CIRCULATORY-MALFORMATIONS

ICD-10-CM Code For Other Congenital Malformations Of Circulatory System: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Congenital Malformations Of Pulmonary And Tricuspid Valves: Group Overview

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ICD-10-CM Q22: Congenital Malformations Of Pulmonary And Tricuspid Valves Overview

ICD-10-CM Code For Congenital Malformations Of Pulmonary And Tricuspid Valves: Group Overview

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ICD-10-CM Q22: Congenital Malformations Of Pulmonary And Tricuspid Valves Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

References

ICD-10-CM Code For Congenital Malformations Of Pulmonary And Tricuspid Valves: Group Overview

Sign up for ICD-10-CM Code For Congenital Malformations Of Pulmonary And Tricuspid Valves: Group Overview policy alerts

ICD-10-CM Q22: Congenital Malformations Of Pulmonary And Tricuspid Valves Overview

ICD-10-CM Code For Congenital Malformations Of Pulmonary And Tricuspid Valves: Group Overview

Sign up for ICD-10-CM Code For Congenital Malformations Of Pulmonary And Tricuspid Valves: Group Overview policy alerts

ICD-10-CM Q22: Congenital Malformations Of Pulmonary And Tricuspid Valves Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which ICD-10-CM code group covers congenital malformations of the pulmonary and tricuspid valves?

What specific conditions are included under `Q22` codes?

Why is precise documentation important when coding `Q22` diagnoses?

Which DRGs are commonly related to `Q22` group diagnoses?

Can `Q22` codes indicate whether a congenital valve condition is stenosis or atresia?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which ICD-10-CM code group covers congenital malformations of the pulmonary and tricuspid valves?

What specific conditions are included under `Q22` codes?

Why is precise documentation important when coding `Q22` diagnoses?

Which DRGs are commonly related to `Q22` group diagnoses?

Can `Q22` codes indicate whether a congenital valve condition is stenosis or atresia?

References