ICD-10-CM Code For Congenital Malformations Of Posterior Segment Of Eye: Group Overview

The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group Q14 includes congenital malformations of the posterior segment of the eye such as optic nerve hypoplasia, coloboma of retina and choroid, and other developmental anomalies of the retina, choroid, sclera, and optic disc. These ICD-10-CM diagnosis codes are used to document congenital ocular structural abnormalities, capturing anatomic location, laterality, and clinical complexity relevant to visual function and developmental impact. Accurate coding within the ICD-10-CM Q14 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

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ICD-10-CM Q14: Congenital Malformations Of Posterior Segment Of Eye Overview

This group represents congenital structural malformations affecting the posterior segment of the eye, including the retina, choroid, sclera, and optic nerve head. These conditions target ocular development and can lead to visual impairment or blindness when severe. Accurate coding matters for appropriate clinical documentation and supports correct reimbursement and continuity of care.

When to Use

Use a code from this group when a patient is diagnosed with a congenital posterior segment ocular malformation documented by clinical examination or imaging. Codes are selected to reflect the anatomic site, specific malformation, and laterality when available.

ICD-10-CM Codes

6 rows

ICD-10-CM Code	Description
Q14.0	Congenital malformation of vitreous humor
Q14.1	Congenital malformation of retina
Q14.2	Congenital malformation of optic disc
Q14.3	Congenital malformation of choroid
Q14.8	Other congenital malformations of posterior segment of eye
Q14.9	Congenital malformation of posterior segment of eye, unspecified

DRG Codes

2 rows

DRG Code	Description
124	Other Disorders of the Eye with MCC or Thrombolytic Agent
125	Other Disorders of the Eye without MCC

Typical Clinical Scenarios

A newborn is evaluated in the neonatal nursery after a failed red reflex screening and abnormal ocular exam; ophthalmoscopy reveals optic nerve hypoplasia and a small, underdeveloped posterior segment. The infant is referred to pediatric ophthalmology for baseline vision assessment and developmental follow-up, and a congenital posterior segment malformation code is assigned to capture the anatomic anomaly present at birth. Typical codes: Q14.0
A school-age child with lifelong reduced visual acuity and strabismus is seen for chronic low vision services; review of prior records and retinal imaging demonstrates coloboma involving the retina and choroid contributing to the visual deficit. Because the structural posterior segment defect is congenital and explains the persistent visual impairment, a congenital posterior segment malformation code for coloboma is used. Typical codes: Q14.2, Q14.3
An adult presents to ophthalmology for evaluation of progressive visual field loss and is found to have a congenital malformation of the vitreous and retina that predisposes to recurrent retinal detachment; the visit documents the congenital posterior segment anomaly as a comorbidity impacting management and surgical planning. Coding reflects the underlying congenital posterior segment malformation in addition to the acquired complications. Typical codes: Q14.1, Q14.8

ICD-10-CM Code For Congenital Malformations Of Eyelid Lacrimal Apparatus And Orbit: Group Overview

Q11-ANOPHTHALMOS-MICROPHTHALMOS-MACROPHTHALMOS

ICD-10-CM Code For Anophthalmos Microphthalmos And Macrophthalmos: Group Overview

Q13-CONGENITAL-MALFORMATIONS-ANTERIOR-SEGMENT

ICD-10-CM Code For Congenital Malformations Of Anterior Segment Of Eye: Group Overview

Q15-OTHER-CONGENITAL-MALFORMATIONS-OF-EYE

ICD-10-CM Code For Other Congenital Malformations Of Eye: Group Overview

Q16-CONGENITAL-MALFORMATIONS-OF-EAR

ICD-10-CM Code For Congenital Malformations Of Ear Causing Impairment Of Hearing: Group Overview

Q17-OTHER-CONGENITAL-MALFORMATIONS-OF-EAR

ICD-10-CM Code For Other Congenital Malformations Of Ear: Group Overview

Q18-OTHER-CONGENITAL-MALFORMATIONS-FACE-NECK

ICD-10-CM Code For Other Congenital Malformations Of Face And Neck: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

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When to Use

ICD-10-CM Codes

6 rows

ICD-10-CM Code	Description
Q14.0	Congenital malformation of vitreous humor
Q14.1	Congenital malformation of retina
Q14.2	Congenital malformation of optic disc
Q14.3	Congenital malformation of choroid
Q14.8	Other congenital malformations of posterior segment of eye
Q14.9	Congenital malformation of posterior segment of eye, unspecified

DRG Codes

2 rows

DRG Code	Description
124	Other Disorders of the Eye with MCC or Thrombolytic Agent
125	Other Disorders of the Eye without MCC

Typical Clinical Scenarios

A newborn is evaluated in the neonatal nursery after a failed red reflex screening and abnormal ocular exam; ophthalmoscopy reveals optic nerve hypoplasia and a small, underdeveloped posterior segment. The infant is referred to pediatric ophthalmology for baseline vision assessment and developmental follow-up, and a congenital posterior segment malformation code is assigned to capture the anatomic anomaly present at birth. Typical codes: Q14.0
A school-age child with lifelong reduced visual acuity and strabismus is seen for chronic low vision services; review of prior records and retinal imaging demonstrates coloboma involving the retina and choroid contributing to the visual deficit. Because the structural posterior segment defect is congenital and explains the persistent visual impairment, a congenital posterior segment malformation code for coloboma is used. Typical codes: Q14.2, Q14.3
An adult presents to ophthalmology for evaluation of progressive visual field loss and is found to have a congenital malformation of the vitreous and retina that predisposes to recurrent retinal detachment; the visit documents the congenital posterior segment anomaly as a comorbidity impacting management and surgical planning. Coding reflects the underlying congenital posterior segment malformation in addition to the acquired complications. Typical codes: Q14.1, Q14.8

ICD-10-CM Code For Congenital Malformations Of Eyelid Lacrimal Apparatus And Orbit: Group Overview

Q11-ANOPHTHALMOS-MICROPHTHALMOS-MACROPHTHALMOS

ICD-10-CM Code For Anophthalmos Microphthalmos And Macrophthalmos: Group Overview

Q13-CONGENITAL-MALFORMATIONS-ANTERIOR-SEGMENT

ICD-10-CM Code For Congenital Malformations Of Anterior Segment Of Eye: Group Overview

Q15-OTHER-CONGENITAL-MALFORMATIONS-OF-EYE

ICD-10-CM Code For Other Congenital Malformations Of Eye: Group Overview

Q16-CONGENITAL-MALFORMATIONS-OF-EAR

ICD-10-CM Code For Congenital Malformations Of Ear Causing Impairment Of Hearing: Group Overview

Q17-OTHER-CONGENITAL-MALFORMATIONS-OF-EAR

ICD-10-CM Code For Other Congenital Malformations Of Ear: Group Overview

Q18-OTHER-CONGENITAL-MALFORMATIONS-FACE-NECK

ICD-10-CM Code For Other Congenital Malformations Of Face And Neck: Group Overview

Frequently Asked Questions

References

1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.

Published by

Trek Health powers OpenPayer with a leading commercial payer intelligence platform, seamlessly converting fragmented payer data into actionable insights for provider organizations.

ICD-10-CM Code For Congenital Malformations Of Posterior Segment Of Eye: Group Overview

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ICD-10-CM Q14: Congenital Malformations Of Posterior Segment Of Eye Overview

ICD-10-CM Code For Congenital Malformations Of Posterior Segment Of Eye: Group Overview

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ICD-10-CM Q14: Congenital Malformations Of Posterior Segment Of Eye Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

References

ICD-10-CM Code For Congenital Malformations Of Posterior Segment Of Eye: Group Overview

Sign up for ICD-10-CM Code For Congenital Malformations Of Posterior Segment Of Eye: Group Overview policy alerts

ICD-10-CM Q14: Congenital Malformations Of Posterior Segment Of Eye Overview

ICD-10-CM Code For Congenital Malformations Of Posterior Segment Of Eye: Group Overview

Sign up for ICD-10-CM Code For Congenital Malformations Of Posterior Segment Of Eye: Group Overview policy alerts

ICD-10-CM Q14: Congenital Malformations Of Posterior Segment Of Eye Overview

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in ICD-10-CM code group `Q14`?

What specific codes are listed under the `Q14` group and what do they represent?

Why is accurate coding within `Q14` important for clinical documentation and reimbursement?

Which DRGs are related to disorders of the eye that may include `Q14` diagnoses?

How do `Q14` codes capture details relevant to patient care and claims?

References

When to Use

ICD-10-CM Codes

DRG Codes

Typical Clinical Scenarios

Related Codes

Which conditions are included in ICD-10-CM code group `Q14`?

What specific codes are listed under the `Q14` group and what do they represent?

Why is accurate coding within `Q14` important for clinical documentation and reimbursement?

Which DRGs are related to disorders of the eye that may include `Q14` diagnoses?

How do `Q14` codes capture details relevant to patient care and claims?

References