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    OpenPayerBilling CodesCoagulation defects, purpura and other hemorrhagic conditionsICD-10-CM d66-hereditary-factor-viii-deficiency
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    ICD-10-CM Code For Hereditary Factor VIII Deficiency: Group Overview

    The International Classification of Diseases, Tenth Revision, Clinical Modification (ICD-10-CM) code group D66 includes hereditary factor VIII deficiency diagnoses such as hemophilia A, covering congenital deficiencies of coagulation factor VIII that cause bleeding diathesis. These ICD-10-CM diagnosis codes are used to document clinical scenarios including bleeding severity, frequency of bleeding episodes, and complications such as joint or intracranial hemorrhage, capturing disease severity, organ involvement, or clinical complexity relevant to this group. Accurate coding within the ICD-10-CM D66 group supports proper claim adjudication, complete clinical documentation, and appropriate reimbursement.

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    ICD-10-CM D66: Hereditary Factor VIII Deficiency Overview

    Hereditary factor VIII deficiency represents congenital hemophilia A caused by a deficiency of clotting factor VIII affecting the coagulation system. These diagnoses target bleeding disorders that primarily impact hemostasis and can lead to spontaneous or trauma-related hemorrhage. Accurate coding matters for clinical records and reimbursement because it documents severity, treatment needs, and justification for clotting factor products and services.

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    When to Use

    Use a code from this group when a patient has a documented diagnosis of congenital factor VIII deficiency or hemophilia A confirmed by laboratory testing or specialist documentation. Codes from this group are appropriate for encounters addressing bleeding episodes, prophylactic or replacement therapy, and management of complications related to factor VIII deficiency.

    ICD-10-CM Codes

    1 rows

    ICD-10-CM CodeDescription
    D66Hereditary factor VIII deficiency

    DRG Codes

    1 rows

    DRG CodeDescription
    813Coagulation Disorders

    Typical Clinical Scenarios

    • A young male infant presents to the emergency department with soft tissue swelling and prolonged bleeding after circumcision; parents report frequent bruising and a family history of bleeding disorders. Laboratory studies show markedly reduced factor VIII activity with normal von Willebrand factor levels, leading to assignment of a diagnosis from this group for hereditary factor VIII deficiency. Typical codes: D66.
    • An adolescent male with a known history of lifelong easy bruising and recurrent hemarthroses is seen in hematology clinic for ongoing management and prophylactic infusion planning; factor assays confirm severe congenital deficiency of factor VIII. The chronic nature of his coagulation disorder and documentation of hereditary origin prompt use of a diagnosis from this group on outpatient problem lists and visit coding. Typical codes: D66.
    • An adult female presents to labor and delivery with postpartum hemorrhage after an uncomplicated vaginal delivery; workup reveals an undiagnosed mild inherited factor VIII deficiency unmasked by the hemostatic stress of childbirth. Because the bleeding is due to a congenital factor VIII deficiency identified during the acute obstetric complication, a code from this group is assigned to capture the underlying hereditary coagulation defect contributing to the hemorrhage. Typical codes: D66.

    Related Codes

    D65-DISSEMINATED-INTRAVASCULAR-COAGULATION

    ICD-10-CM Code For Disseminated Intravascular Coagulation Defibrination Syndrome: Group Overview

    D67-HEREDITARY-FACTOR-IX-DEFICIENCY

    ICD-10-CM Code For Hereditary Factor IX Deficiency: Group Overview

    D68-OTHER-COAGULATION-DEFECTS

    ICD-10-CM Code For Other Coagulation Defects: Group Overview

    D69-PURPURA-AND-HEMORRHAGIC-CONDITIONS

    ICD-10-CM Code For Purpura And Other Hemorrhagic Conditions: Group Overview

    Frequently Asked Questions

    References

    1. 1.CPT® Codes and Descriptions. AAPC. Retrieved Aug 11, 2026.Maintains the CPT code set's official descriptions and guidelines, licensed from the American Medical Association, used as the definitional source for CPT codes on this page.
    2. 2.HCPCS Quarterly Update. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's quarterly release of HCPCS Level II codes and short/long descriptors, the source for HCPCS code definitions and update history.
    3. 3.ICD-10-CM Full Code List. Centers for Medicare & Medicaid Services (CMS). Retrieved Aug 11, 2026.CMS's complete ICD-10-CM diagnosis code list, used to cross-reference diagnosis codes associated with this procedure or service.
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