ACC AUC – CHD: ASD/PAPVC/PFO
ACC AUC–based coverage criteria for transthoracic echocardiography (TTE) in congenital heart disease (CHD). The following condition-specific surveillance indications and timing are considered when determining medical necessity for non-stress TTE (with or without 3D; with contrast as needed). Scores/ratings are the ACC AUC score (1-9) and rating (A = Appropriate, M = May be Appropriate, R = Rarely Appropriate) and reflect the AUC recommendations.
Table 1: CHD — Patent Foramen Ovale (PFO), Atrial Septal Defect (ASD), Partial Anomalous Pulmonary Venous Connection (PAPVC)
- Routine surveillance of an asymptomatic patient with PFO: TTE = 1/R; TTE with contrast = 1/R.
- Routine surveillance (1-2 years) in asymptomatic patient with small ASD or PAPVC (single pulmonary vein): TTE = 4/M; TTE with contrast = Not rated.
- Routine surveillance (3-5 years) in asymptomatic patient with small ASD or PAPVC (single pulmonary vein): TTE = 7/A; TTE with contrast = Not rated.
- Evaluation due to change in clinical status and/or new concerning signs or symptoms: TTE = 8/9 = A; TTE with contrast = Not rated/5/M depending on specific scenario.
- Evaluation to determine method of closure of isolated secundum ASD: TTE = 8/9 = A; TTE with contrast = Not rated/4/M as indicated.
- Pre- and postprocedural surveillance: routine postprocedural evaluation within 30 days = 8/9 = A; selected routine follow-up timing after device/surgical closure at 1 week, 1 month, 3-6 months, 1 year and longer intervals per AUC (ratings vary: many 8/9 = A; some Not rated or lower ratings for contrast).
ACC AUC – CHD: Ventricular Septal Defects
Table 2: CHD — Ventricular Septal Defects (VSD). Condition-specific surveillance and evaluation indications.
Routine surveillance (1-2 years) in asymptomatic child with small muscular VSD: TTE = 3/R.
Routine surveillance (3-5 years) in asymptomatic child or adult with small muscular VSD: TTE = 7/A.
Routine surveillance (1-2 years) in asymptomatic child with small non-muscular VSD: TTE = 7/A (child) and adult 8/A as specified.
Routine surveillance (1-3 months) in infant with ≥ moderate VSD on medical management: TTE = 9/A.
Evaluation due to change in clinical status or prior to planned repair: TTE = 9/A.
Postprocedural routine postprocedural evaluation (within 30 days): TTE = 9/A.
Routine surveillance timing after surgical or device closure (within first year and then annually or 2-3 years) per AUC; ratings vary (commonly 8-9/A).
ACC AUC – CHD: Atrioventricular Septal Defects
Table 3: CHD — Atrioventricular Septal Defects (AVSD). Indications and surveillance timing.
Routine surveillance (3-6 months) in asymptomatic infant: TTE = 9/A.
Routine surveillance (1-2 years) in asymptomatic child: TTE = 9/A.
Evaluation due to change in clinical status, evaluation prior to planned repair, and routine postprocedural evaluation within 30 days: TTE = 9/A.
Routine longer-term surveillance after repair: within 1 year and then 1–3 years (TTE = 9/A) when no or mild sequelae; increased frequency (3-12 months) for significant residual shunt, valvular/ventricular dysfunction, arrhythmias, or pulmonary hypertension (TTE = 9/A).
ACC AUC – CHD: Patent Ductus Arteriosus
Table 4: CHD — Patent Ductus Arteriosus (PDA). Surveillance by age, severity, and postprocedural status.
Routine surveillance (3-5 years) in asymptomatic patient with trivial, silent PDA: TTE = 3/R.
Routine surveillance (3-6 months) in infant with ≥ moderate PDA: TTE = 9/A.
Routine surveillance (3-6 months) in infant with small audible PDA until closure: TTE = 7/A.
Routine surveillance (1-2 years) in infant/child with small audible PDA until closure: TTE = 8/A.
Routine surveillance (3-5 years) in adult with small PDA: TTE = 9/A.
Evaluation due to change in clinical status or prior to planned repair: TTE = 9/A.
Postprocedural routine postprocedural evaluation within 30 days: TTE = 9/A. Routine longer-term surveillance after closure varies by device vs surgical repair and sequelae (ratings vary).
ACC AUC – CHD: Total Anomalous Pulmonary Venous Connection
Table 5: CHD — Total Anomalous Pulmonary Venous Connection (TAPVC). Indications for evaluation and routine surveillance.
Evaluation due to change in clinical status and/or new concerning signs or symptoms: TTE = 9/A.
Evaluation prior to planned repair: TTE = 9/A.
Routine postprocedural evaluation within 30 days: TTE = 9/A.
Routine surveillance (3-6 months) in asymptomatic infant with no or mild sequelae: TTE = 8/A.
Routine surveillance (1-2 years) in asymptomatic child with no or mild sequelae: TTE = 8/A.
ACC AUC – CHD: Eisenmenger Syndrome / Pulmonary Hypertension
Table 6: CHD — Eisenmenger Syndrome (ES) and pulmonary hypertension associated with CHD. Surveillance and evaluation guidance.
Initial evaluation with suspicion of ES: TTE = 9/A.
Evaluation due to change in clinical status or change in PH-targeted therapy: TTE = 9/A.
Routine surveillance: children—3 months when stable (some ratings 6/M, 9/A depending on age); adults—6-12 months when stable (ratings include 3/R and 9/A depending on context).
For postoperative pulmonary hypertension or suspected PH following CHD surgery: initial evaluation and changes in therapy: TTE = 9/A; routine surveillance intervals per age and stability (3 months to 6-12 months) with ratings as specified.
ACC AUC – CHD: Ebstein Anomaly / Tricuspid Valve
Table 7: CHD — Ebstein Anomaly and Tricuspid Valve Dysplasia. Surveillance by age, symptom status, TR severity, and ventricular function.
Routine surveillance (1-2 years) in asymptomatic infant/child with mild tricuspid regurgitation (TR): TTE = 9/A; TTE with contrast = Not rated.
Routine surveillance (3-5 years) in asymptomatic adult with mild TR: TTE = 9/A; TTE with contrast = 5/M.
Routine surveillance (3-6 months) in asymptomatic infant with ≥ moderate TR without hypoxemia: TTE = 9/A; contrast not rated.
Routine surveillance (6-12 months) in asymptomatic patient with ≥ moderate TR and previously stable RV size/function without hypoxemia: TTE = 9/A; TTE with contrast = 4/M.
Evaluation due to change in clinical status or new concerning signs/symptoms: TTE = 9/A; TTE with contrast = 7/A where indicated.
Evaluation of ASD for device closure in patient with mild/moderate TR and RV enlargement: TTE = 9/A.
ACC AUC – CHD: Pulmonary Stenosis
Table 8: CHD — Pulmonary Stenosis (PS). Surveillance by age and PS severity.
Routine surveillance (3-6 months) in asymptomatic infant with mild PS: TTE = 8/A.
Routine surveillance (1-2 years) in asymptomatic child with mild PS: TTE = 8/A.
Routine surveillance (3-5 years) in asymptomatic adult with mild PS: TTE = 9/A.
Routine surveillance (3-6 months) in asymptomatic infant with ≥ moderate PS: TTE = 9/A.
Routine surveillance (1-2 years) in asymptomatic child or adult with ≥ moderate PS: TTE = 9/A.
Routine surveillance (3-5 years) in asymptomatic adult with PS and pulmonary artery dilation: TTE = 9/A.
Evaluation for change in clinical status, pre-repair evaluation, and routine postprocedural within 30 days: TTE = 9/A.
Routine surveillance intervals for sequelae and symptomatic patients vary (3-12 months) with TTE = 9/A.
ACC AUC – CHD: Pulmonary Atresia with Intact Ventricular Septum
Table 9: CHD — Pulmonary Atresia with Intact Ventricular Septum. Evaluation and surveillance guidance.
Evaluation prior to planned repair: TTE = 9/A.
Routine postprocedural evaluation (within 30 days): TTE = 9/A.
Routine surveillance (1-3 months) in asymptomatic patient: TTE = 9/A.
Routine surveillance (3-6 months) in asymptomatic infant, and 1-2 years in asymptomatic child with no or mild sequelae: TTE = 9/A.
Routine surveillance intervals for moderate/severe sequelae and symptomatic patients: TTE = 9/A with 3-12 month follow-up where indicated.
ACC AUC – CHD: Mitral Valve Disease
Table 10: CHD — Mitral Valve Disease (including congenital mitral stenosis [MS], mitral regurgitation [MR], mitral valve prolapse). Surveillance by age, severity, ventricular function, and prosthetic valve status.
Routine surveillance (1-4 weeks) in infant <3 months with any degree of MS: TTE = 8/A.
Routine surveillance (3-6 months) in infant ≥3 months with mild MS: TTE = 8/A; (1-3 months) for ≥ moderate MS: TTE = 9/A.
Routine surveillance (6-12 months) in asymptomatic infant with mild MR: TTE = 9/A; (1-3 months) for infant with ≥ moderate MR: TTE = 9/A.
Routine surveillance (2-5 years) in child with mild MR and normal LV size/function: TTE = 9/A.
Routine surveillance intervals for prosthetic mitral valves: annually or more frequent depending on dysfunction (many entries TTE = 9/A).
ACC AUC – CHD: LVOT / Aortic Valve Disease and Aortic Dilation
Table 11: CHD — Left Ventricular Outflow Tract (LVOT) lesions and Aortic Valve disease. Surveillance by lesion, age, severity, and aortic dilation.
Routine surveillance (1-3 months) in infant with any degree subvalvular aortic stenosis (AS) and ≤ mild AR: TTE = 9/A.
Routine surveillance (1-2 years) in child/adult with mild subvalvular AS and no AR: TTE = 9/A.
Routine surveillance (6-12 months) in child/adult with ≥ moderate subvalvular AS and/or ≤ mild AR: TTE = 9/A.
Routine surveillance (3-5 years) in asymptomatic adult with ≥ moderate subvalvular AS: TTE = 9/A.
Infant surveillance timing by degree of AS/AR: 1-4 weeks to 1-3 months depending on severity (many entries TTE = 9/A).
Bicuspid aortic valve with aortic dilation: surveillance intervals for aortic sinus/ascending aorta per AUC (e.g., 6-12 months for increasing z-scores, 2-3 years for stable mild dilation); many entries TTE = 9/A or 3/R depending on specific scenario.
Postoperative and postprocedural routine evaluation within 30 days: TTE = 9/A.
ACC AUC – CHD: Aortic Coarctation / Interrupted Aortic Arch
Table 12: CHD — Aortic Coarctation and Interrupted Aortic Arch. Surveillance and post-intervention follow-up guidance.
Routine surveillance (3-6 months) in infant with mild aortic coarctation without PDA: TTE = 9/A.
Routine surveillance (1-2 years) in child/adult with mild coarctation: TTE = 9/A.
Routine surveillance (3-6 months) within first year following repair in asymptomatic patient with no or mild sequelae: ratings vary (some entries Not rated; many 9/A for later intervals).
Routine surveillance (6-12 months) within first year following catheter-based intervention: Not rated in some entries; later surveillance at 6 months and then 1-2 years after first year: TTE = 9/A.
Routine surveillance (3-5 years) to evaluate for aortic arch aneurysms, in-stent stenosis, stent fracture, or endoleak: Not rated for some entries; escalate for symptoms (3-12 months) TTE = 9/A.
ACC AUC – CHD: Coronary Anomalies
Table 13: CHD — Coronary Anomalies. Surveillance by anomaly type and fistula size.
Routine surveillance (annually) in asymptomatic patient with anomalous right coronary artery from left aortic sinus: TTE = 3/R; routine surveillance (2-5 years) TTE = 7/A.
Routine surveillance (annually) in asymptomatic patient with small coronary fistula: TTE = 3/R; routine surveillance (2-5 years) TTE = 8/A.
Routine surveillance (1-2 years) in asymptomatic patient with moderate or large coronary fistula: TTE = 9/A.
Evaluation due to change in clinical status, pre-repair evaluation, and routine postprocedural evaluation within 30 days: TTE = 9/A.
Routine surveillance (1-3 months) within first year following repair: TTE = 7/A; routine longer-term surveillance intervals depend on sequelae and residual dysfunction.
ACC AUC – CHD: Tetralogy of Fallot
Table 14: CHD — Tetralogy of Fallot (TOF). Surveillance before and after repair and by sequelae.
Routine surveillance (1-3 months) in infant before complete repair and following interim procedures (valvuloplasty, RVOT stenting, shunt placement): TTE = 9/A.
Postoperative initial repair surveillance within 30 days: TTE = 9/A.
Routine surveillance annually in asymptomatic patient with no or mild sequelae or pulmonary regurgitation of any severity: TTE = 9/A.
Routine surveillance (6-12 months) in patients with valvular dysfunction other than pulmonary valve, RVOT obstruction, branch pulmonary artery stenosis, arrhythmias, or RV-to-PA conduit: TTE = 9/A.
Routine surveillance (2-3 years) for patients with pulmonary regurgitation and preserved ventricular function: some entries Not rated; for other sequelae interval commonly 1-3 years or 6-12 months depending on dysfunction (TTE = 9/A where noted).
Evaluation prior to planned pulmonary valve replacement and postprocedural follow-up (1 year, 1 and 6 months after transcatheter replacement) per AUC: TTE = 9/A.
ACC AUC – CHD: Double Outlet Right Ventricle
Table 15: CHD — Double Outlet Right Ventricle (DORV). Surveillance and postoperative follow-up.
Routine surveillance (1-3 months) in infant with balanced circulation: TTE = 9/A.
Routine surveillance (3-6 months) in child with balanced circulation: TTE = 9/A.
Evaluation due to change in clinical status or prior to planned repair: TTE = 9/A.
Routine postprocedural evaluation within 30 days: TTE = 9/A.
Routine surveillance (6 months within first year) after repair in asymptomatic infant/child with no or mild sequelae: TTE = 9/A; longer-term intervals (1-2 years) in asymptomatic patients with no or mild sequelae: TTE = 9/A.
More frequent surveillance (3-12 months) for valvular/ventricular dysfunction, RV/LV outflow obstruction, branch pulmonary artery stenosis, arrhythmias, or conduits: TTE = 9/A.
ACC AUC – CHD: D-Loop Transposition of the Great Arteries
Table 16: CHD — D-Loop Transposition of the Great Arteries (D-Loop TGA). Indications for evaluation, postoperative surveillance, and coronary imaging consideration.
Evaluation due to change in clinical status or prior to planned repair: TTE = 9/A.
Postoperative arterial switch: routine postoperative evaluation within 30 days: TTE = 9/A.
Routine surveillance (1-3 months) in asymptomatic infant with moderate sequelae: TTE = 9/A; (3-6 months) for infants with no or mild sequelae: TTE = 9/A.
Routine surveillance (3-12 months) in older children/adults with ≥ moderate valvular/ventricular dysfunction, outflow obstruction, branch pulmonary artery stenosis, or arrhythmias: TTE = 9/A.
Evaluation for coronary imaging in an asymptomatic patient: TTE = Not rated (alternative modalities may be considered per AUC).
ACC AUC – CHD: ccTGA
Table 17: CHD — Congenitally Corrected Transposition of the Great Arteries (ccTGA). Surveillance recommendations.
Evaluation due to change in clinical status: TTE = 9/A; TTE with contrast entries often Not rated.
Routine surveillance (3-6 months) in asymptomatic infant: TTE = 9/A (contrast Not rated).
Routine surveillance (1-2 years) in patient with < moderate systemic AV valve regurgitation: TTE = 9/A; contrast Not rated.
Routine surveillance (6-12 months) in patient with ≥ moderate systemic AV valve regurgitation: TTE = 9/A; contrast Not rated.
Routine surveillance (3-5 years) in asymptomatic patient: TTE = 9/A (contrast Not rated).
Evaluation prior to planned repair and routine postprocedural follow-up per AUC: TTE = 9/A.
ACC AUC – CHD: Truncus Arteriosus
Table 18: CHD — Truncus Arteriosus. Indications for evaluation, postoperative, and surveillance.
Evaluation due to change in clinical status or prior to planned repair: TTE = 9/A.
Routine postprocedural evaluation within 30 days: TTE = 9/A.
Routine surveillance (1-3 months) within first year after repair in asymptomatic patient: TTE = 9/A.
Routine surveillance (6-12 months) after first year in asymptomatic child/adult with no or mild sequelae: TTE = 9/A.
Routine surveillance intervals (3-5 years) for stable asymptomatic patients may be Not rated in some entries; escalate frequency for moderate stenosis/regurgitation or residual defects (3-12 months) TTE = 9/A.
ACC AUC – CHD: Single-Ventricle Heart Disease
Table 19: CHD — Single-Ventricle Heart Disease. Surveillance and timing around staged palliation.
Routine surveillance (1-4 weeks) in patient with balanced systemic and pulmonary circulation not requiring neonatal surgery: TTE = 9/A (contrast Not rated).
Evaluation due to change in clinical status or prior to planned surgical palliation: TTE = 9/A.
Postprocedural (Stage 1 palliation) routine postprocedural evaluation within 30 days: TTE = 9/A.
Routine surveillance (6 months within first year) after repair in asymptomatic infant/child with no or mild sequelae: TTE = 9/A. Longer-term surveillance intervals vary based on stage, residual lesions, and clinical status; more frequent imaging (3-12 months) for significant sequelae or symptoms.